Bronchopulmonary Sequestration
Hydrops Fetalis
Bronchopulmonary Dysplasia
Aspergillosis, Allergic Bronchopulmonary
Angiography, Digital Subtraction
Ventilation-Perfusion Ratio
Technetium Tc 99m Aggregated Albumin
Pulmonary Artery
Diagnosis of pulmonary sequestration by spiral CT angiography. (1/92)
The diagnosis of pulmonary sequestration traditionally requires arteriography to identify abnormal systemic vessels feeding the abnormal portion of the lung. Non-invasive imaging techniques have recently been used to replace arteriography. Conventional computed tomographic (CT) scanning is, however, at a disadvantage because of its inability to obtain multiplanar images. The combination of slip ring CT scanning and computerised three-dimensional reconstruction (spiral CT angiography) can be used to visualise the anatomical detail of a wide range of vessels within the lung. Four cases of pulmonary sequestration are reported which were successfully diagnosed using spiral CT angiography. Spiral CT scanning allows simultaneous imaging of anomalous vessels and lung parenchyma in a single examination and is particularly useful in the diagnosis and assessment of pulmonary sequestration. (+info)Direct intrauterine fetal therapy in a case of bronchopulmonary sequestration associated with non-immune hydrops fetalis. (2/92)
Bronchopulmonary sequestration associated with non-immune hydrops fetalis is generally recognized as a uniformly fatal fetal condition without fetal surgical intervention. We describe here the first case of such a condition treated successfully with direct intrauterine fetal therapy using digoxin and frusemide. (+info)Management of antenatally diagnosed pulmonary sequestration associated with congenital cystic adenomatoid malformation. (3/92)
BACKGROUND: Sequestration with associated cystic adenomatoid malformation is rare. A study was undertaken to determine whether pulmonary sequestration associated with congenital cystic adenomatoid malformation has a more favourable natural history than that of sequestration without associated cystic adenomatoid malformation. METHODS: An outline of the postnatal work up leading to the management of extralobar or intralobar pulmonary sequestration with congenital cystic adenomatoid malformation diagnosed antenatally as pulmonary malformation is presented and the indications for surgical intervention are discussed. RESULTS: In five infants in whom an antenatal ultrasound scan had detected a congenital lung malformation at 18-19 weeks gestation a final diagnosis of extralobar or intralobar pulmonary sequestration with congenital cystic adenomatoid malformation was made postnatally. Postnatal ultrasound and computerised axial tomographic scans confirmed the diagnosis of sequestration by delineating anomalous vascular supply. Cystic changes were also observed in the basal area of the sequestration in all patients. Four children remained asymptomatic and one infant presented at 10 months of age with pneumonia. The mean age at surgical resection was 6.8 months (range 2-10). Histopathological examination confirmed intralobar pulmonary sequestration with associated Stocker type 2 congenital cystic adenomatoid malformation in two patients and extralobar pulmonary sequestration with associated Stocker type 2 congenital cystic adenomatoid malformation in three patients. The mean period of follow up was four years (range 1-8). The children remain well and are developing normally. CONCLUSIONS: The importance of seeking an anomalous blood supply in children with congenital lung lesions is emphasised. Pulmonary sequestration and congenital cystic adenomatoid malformation probably share a common embryogenesis despite diverse morphology. The natural history of antenatally diagnosed lung masses is variable. Early postnatal surgical resection of pulmonary sequestration with cystic adenomatoid malformation is recommended. Surgical excision should be conservative, sparing the normal lung parenchyma. (+info)A familial case of pulmonary arterial sequestration. (4/92)
The cases of a mother and infant son are reported, both with a rare type of pulmonary sequestration where the arterial supply to the lung arises from the systemic circulation. This is a familial case of arterial sequestration. In both patients, the lung parenchyma was radiologically normal. (+info)Primary lymphoepithelioma-like carcinoma within an intralobular pulmonary sequestration. (5/92)
A 31-yr-old Chinese female, a nonsmoker, presented with digital clubbing and coughing. Diagnostic evaluation revealed a pulmonary sequestration in the left lower lobe. During surgery a tumour was discovered, which turned out to be a lymphoepithelioma-like carcinoma. These tumours are mainly found in Asians, and are associated with the Epstein Barr virus and not with smoking. They are thought to have a better prognosis and to be more chemosensitive. The need for surgical treatment of pulmonary sequestration and the recognition of lymphoepithelioma-like carcinoma as a distinct clinicopathological entity is emphasized. (+info)Contrast enhanced MR angiography in pulmonary sequestration. (6/92)
OBJECTIVE: To evaluate the feasibility of contrast enhanced three-dimensional (3D) magnetic resonance angiography (MRA) in identifying the systemic blood supply in pulmonary sequestration. METHODS: Three patients who were suspected of pulmonary sequestration were examined by contrast enhanced 3D MRA. MR images were compared with surgical findings. RESULTS: Contrast enhanced 3D MRA clearly demonstrated systemic arteries from the descending thoracic aorta supplying the basilar segments of the lower lobe in each case. Pulmonary veins from these segments, which drained into the left atrium in two cases, were also detected. MRA images were consistent with those observed in surgery. CONCLUSION: Contrast enhanced 3D MRA allows accurate diagnosis of pulmonary sequestration and may obviate the need for more invasive investigations. (+info)Intralobar pulmonary sequestration presenting increased serum CA19-9 and CA125. (7/92)
A 39-year-old man was admitted to our hospital for further evaluation of a consolidated shadow and clarification of the cause of serum tumor marker elevation (CA19-9 496.2 U/ml, CA125 160.6 U/ml). Chest computed tomography revealed a well-defined homogeneous nodule in the left S(10). Angiography showed one aberrant artery, branching from the ascending aorta. Intralobar pulmonary sequestration was diagnosed and the sequestrated lung was resected. Microscopic findings of the sequestrated lung showed a mucus-containing cystically dilated bronchus, which was covered with ciliated cylindrical epithelium. Immunohistochemical staining showed positive staining for CA19-9 and CA125 in both the ciliated cylindrical epithelium and mucus. Serum values of tumor markers returned to their normal range after surgery. (+info)Pulmonary sequestration associated by Mycobacterium intracellulare infection. (8/92)
A case of a 29-year-old woman with intralobar pulmonary sequestration infected with Mycobacterium intracellulare is presented. A chest CT scan revealed a density in the posterior segment of the left lower lobe, and an acid-fast bacillus sputum culture yielded Mycobacterium intracellulare. After 3 months of treatment with clarithromycin, streptomycin, rifampicin and ethambutol, the patient underwent partial resection of the left lower lobe. At the 6-month follow-up the patient's clinical status is excellent. A review of the literature revealed only three case reports of pulmonary sequestration associated with Mycobacterium avium-intracellulare complex infection. (+info)Bronchopulmonary sequestration is a rare birth defect of the lungs, in which a mass of abnormal lung tissue develops that doesn't function and isn't connected to the tracheobronchial tree (the airways that lead to the lungs). This means that the abnormal tissue receives its blood supply from an anomalous systemic artery instead of the normal pulmonary circulation. The mass may be located within the lung (intralobar sequestration) or outside the lung (extralobar sequestration), and it can occur on either side of the chest.
Intralobar sequestrations are more common than extralobar sequestrations, accounting for about 75% of cases. They are usually found in adults and are located within a normal lung tissue. Extralobar sequestrations, on the other hand, are typically detected earlier in life (often as an incidental finding during prenatal ultrasound) and are surrounded by their own pleural lining, which can make them appear separate from the normal lung tissue.
Symptoms of bronchopulmonary sequestration may include recurrent respiratory infections, coughing up blood (hemoptysis), shortness of breath, or chest pain. Treatment usually involves surgical removal of the abnormal tissue to prevent complications such as infection, bleeding, or the development of malignancy.
Hydrops Fetalis is a serious condition characterized by the accumulation of excessive fluid in two or more fetal compartments, including the abdomen (ascites), around the heart (pericardial effusion), and/or within the lungs (pleural effusion). This accumulation can also affect the skin, causing it to become edematous. Hydrops Fetalis is often associated with various underlying causes, such as chromosomal abnormalities, congenital infections, genetic disorders, and structural defects that impair the fetus's ability to maintain fluid balance. In some cases, the cause may remain unknown. The prognosis for Hydrops Fetalis is generally poor, with a high mortality rate, although early detection and appropriate management can improve outcomes in certain situations.
Bronchopulmonary dysplasia (BPD) is a chronic lung disease that primarily affects premature infants. It is defined as the need for supplemental oxygen at 28 days of life or beyond, due to abnormal development and injury to the lungs.
The condition was first described in the 1960s, following the introduction of mechanical ventilation and high concentrations of oxygen therapy for premature infants with respiratory distress syndrome (RDS). These treatments, while lifesaving, can also cause damage to the delicate lung tissue, leading to BPD.
The pathogenesis of BPD is complex and involves an interplay between genetic factors, prenatal exposures, and postnatal injury from mechanical ventilation and oxygen toxicity. Inflammation, oxidative stress, and impaired lung development contribute to the development of BPD.
Infants with BPD typically have abnormalities in their airways, alveoli (air sacs), and blood vessels in the lungs. These changes can lead to symptoms such as difficulty breathing, wheezing, coughing, and poor growth. Treatment may include oxygen therapy, bronchodilators, corticosteroids, diuretics, and other medications to support lung function and minimize complications.
The prognosis for infants with BPD varies depending on the severity of the disease and associated medical conditions. While some infants recover completely, others may have long-term respiratory problems that require ongoing management.
Allergic bronchopulmonary aspergillosis (ABPA) is a medical condition characterized by an hypersensitivity reaction to the fungus Aspergillus species, most commonly A. fumigatus. It primarily affects the airways and lung tissue. The immune system overreacts to the presence of the fungus, leading to inflammation and damage in the lungs.
The main symptoms of ABPA include wheezing, coughing, production of thick mucus, shortness of breath, and chest tightness. These symptoms are similar to those seen in asthma and other respiratory conditions. Some people with ABPA may also experience fever, weight loss, and fatigue.
Diagnosis of ABPA typically involves a combination of clinical evaluation, imaging studies (such as chest X-rays or CT scans), and laboratory tests (such as blood tests or sputum cultures) to detect the presence of Aspergillus species and elevated levels of certain antibodies.
Treatment for ABPA usually involves a combination of corticosteroids to reduce inflammation and antifungal medications to eradicate the Aspergillus infection. In some cases, immunomodulatory therapies may also be used to help regulate the immune system's response to the fungus.
It is important to note that ABPA can lead to serious complications if left untreated, including bronchiectasis (permanent enlargement of the airways), pulmonary fibrosis (scarring of the lung tissue), and respiratory failure. Therefore, prompt diagnosis and treatment are essential for managing this condition.
A pulmonary embolism (PE) is a medical condition that occurs when a blood clot, often formed in the deep veins of the legs (deep vein thrombosis), breaks off and travels to the lungs, blocking one or more pulmonary arteries. This blockage can lead to various symptoms such as shortness of breath, chest pain, rapid heart rate, and coughing up blood. In severe cases, it can cause life-threatening complications like low oxygen levels, hypotension, and even death if not promptly diagnosed and treated with anticoagulant medications or thrombolytic therapy to dissolve the clot.
Angiography is a medical procedure in which an x-ray image is taken to visualize the internal structure of blood vessels, arteries, or veins. This is done by injecting a radiopaque contrast agent (dye) into the blood vessel using a thin, flexible catheter. The dye makes the blood vessels visible on an x-ray image, allowing doctors to diagnose and treat various medical conditions such as blockages, narrowing, or malformations of the blood vessels.
There are several types of angiography, including:
* Cardiac angiography (also called coronary angiography) - used to examine the blood vessels of the heart
* Cerebral angiography - used to examine the blood vessels of the brain
* Peripheral angiography - used to examine the blood vessels in the limbs or other parts of the body.
Angiography is typically performed by a radiologist, cardiologist, or vascular surgeon in a hospital setting. It can help diagnose conditions such as coronary artery disease, aneurysms, and peripheral arterial disease, among others.
Digital subtraction angiography (DSA) is a medical imaging technique used to visualize the blood vessels and blood flow within the body. It combines the use of X-ray technology with digital image processing to produce detailed images of the vascular system.
In DSA, a contrast agent is injected into the patient's bloodstream through a catheter, which is typically inserted into an artery in the leg and guided to the area of interest using fluoroscopy. As the contrast agent flows through the blood vessels, X-ray images are taken at multiple time points.
The digital subtraction process involves taking a baseline image without contrast and then subtracting it from subsequent images taken with contrast. This allows for the removal of background structures and noise, resulting in clearer images of the blood vessels. DSA can be used to diagnose and evaluate various vascular conditions, such as aneurysms, stenosis, and tumors, and can also guide interventional procedures such as angioplasty and stenting.
The Ventilation-Perfusion (V/Q) ratio is a measure used in respiratory physiology to describe the relationship between the amount of air that enters the alveoli (ventilation) and the amount of blood that reaches the alveoli to pick up oxygen (perfusion).
In a healthy lung, these two processes are well-matched, meaning that well-ventilated areas of the lung also have good blood flow. This results in a V/Q ratio close to 1.0.
However, certain lung conditions such as emphysema or pulmonary embolism can cause ventilation and perfusion to become mismatched, leading to a V/Q ratio that is either higher (ventilation exceeds perfusion) or lower (perfusion exceeds ventilation) than normal. This mismatch can result in impaired gas exchange and lead to hypoxemia (low oxygen levels in the blood).
The V/Q ratio is often used in clinical settings to assess lung function and diagnose respiratory disorders.
Technetium Tc 99m Aggregated Albumin is a radiopharmaceutical preparation used in diagnostic imaging. It consists of radioactive technetium-99m (^99m^Tc) chemically bonded to human serum albumin, which has been aggregated to increase its size and alter its clearance from the body.
The resulting compound is injected into the patient's bloodstream, where it accumulates in the reticuloendothelial system (RES), including the liver, spleen, and bone marrow. The radioactive emission of technetium-99m can then be detected by a gamma camera, producing images that reflect the distribution and function of the RES.
This imaging technique is used to diagnose and monitor various conditions, such as liver disease, inflammation, or tumors. It provides valuable information about the patient's health status and helps guide medical decision-making.
The pulmonary artery is a large blood vessel that carries deoxygenated blood from the right ventricle of the heart to the lungs for oxygenation. It divides into two main branches, the right and left pulmonary arteries, which further divide into smaller vessels called arterioles, and then into a vast network of capillaries in the lungs where gas exchange occurs. The thin walls of these capillaries allow oxygen to diffuse into the blood and carbon dioxide to diffuse out, making the blood oxygen-rich before it is pumped back to the left side of the heart through the pulmonary veins. This process is crucial for maintaining proper oxygenation of the body's tissues and organs.
Sodium Pertechnetate Tc 99m is a radioactive pharmaceutical preparation used in medical diagnostic imaging. It is a technetium-99m radiopharmaceutical, where technetium-99m is a metastable nuclear isomer of technetium-99, which emits gamma rays and has a half-life of 6 hours. Sodium Pertechnetate Tc 99m is used as a contrast agent in various diagnostic procedures, such as imaging of the thyroid, salivary glands, or the brain, to evaluate conditions like inflammation, tumors, or abnormalities in blood flow. It is typically administered intravenously, and its short half-life ensures that the radiation exposure is limited.
Pulmonary sequestration
Congenital pulmonary airway malformation
Hydrops fetalis
EXIT procedure
BPS
List of MeSH codes (C16)
HOXB5
Respiratory disease
What is bronchopulmonary sequestration? | Nicklaus Children's Hospital
Pulmonary Angiography: Practice Essentials, Lung Scintigraphy, Digital Subtraction Pulmonary Angiography
Pulmonary sequestration - Wikipedia
Pediatric Pulmonary Sequestration Workup: Laboratory Studies, Imaging Studies, Procedures
Fetal Care Center at Yale New Haven Children's Hospital
The Fetal Care Center of Southern California - Fetal Care & Diagnostic Center
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Atypical extralobar sequestration: CT-Pathological correlation<...
The thoracic mass: An unusual etiology<...
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Pulmonary35
- BPS, pulmonary sequestration, accessory lung. (nicklauschildrens.org)
- A pulmonary sequestration is a medical condition wherein a piece of tissue that ultimately develops into lung tissue is not attached to the pulmonary arterial blood supply, as is the case in normally developing lung. (wikipedia.org)
- Failure to have a pulmonary sequestration removed can lead to a number of complications. (wikipedia.org)
- These include: Potentially fatal hemorrhage The creation of a left-right shunt, where blood flows in a shortcut through the feed off the aorta Chronic infection with diseases such as Bronchiectasis Tuberculosis Aspergillosis Bronchial carcinoid Bronchogenic squamous cell carcinoma There is still much debate to whether pulmonary sequestration is a congenital problem or acquired through recurrent pulmonary infection. (wikipedia.org)
- It is widely believed that extralobar pulmonary sequestrations are a result of prenatal pulmonary malformation while intralobar pulmonary sequestrations can develop due to recurrent pulmonary infections in adolescents and young adults. (wikipedia.org)
- The most common location is in the posterior basal segment, and nearly two thirds of pulmonary sequestrations appear in the left lung. (wikipedia.org)
- Extralobar sequestration in which the mass is located outside the normal lung and has its own visceral pleuraThe blood supply of 75% of pulmonary sequestrations is derived from the thoracic or abdominal aorta. (wikipedia.org)
- No laboratory studies are needed in pulmonary sequestration. (medscape.com)
- Presence of systemic arteries revealed by chest imaging is the major diagnostic feature of pulmonary sequestration. (medscape.com)
- Flye MW, Conley M, Silver D. Spectrum of pulmonary sequestration. (medscape.com)
- Alivizatos P, Cheatle T, de Leval M, Stark J. Pulmonary sequestration complicated by anomalies of pulmonary venous return. (medscape.com)
- Pulmonary sequestration in infants and children: a 20-year experience and review of the literature. (medscape.com)
- Lung malformations, including congenital pulmonary airway malformations (CPAM, formerly called CCAM) and bronchopulmonary sequestration (BPS), are uncommon disorders that can cause a wide range of problems, including breathing difficulties, recurrent infection, and more rarely, cancer. (mottchildren.org)
- Pulmonary sequestration is an embryonic mass of lung tissue that has no identifiable bronchial communication and that receives its blood supply from 1 or more anomalous systemic arteries. (medscape.com)
- 75% of patients with pulmonary sequestration). (medscape.com)
- Intralobar pulmonary sequestration. (medscape.com)
- Contrast enhanced computed tomography scan (CT) in a 34-year-old female with an extralobar pulmonary sequestration. (medscape.com)
- Contrast enhanced computed tomography angiogram in a 34-year-old female with an extralobar pulmonary sequestration (same patient as in the previous image). (medscape.com)
- The finding of alternative venous drainage patterns separates pulmonary sequestration from other diagnoses, such as infection and tumor, round atelectasis, Bochdalek hernia, and pulmonary infarction. (medscape.com)
- In ILS, sequestrations occur within pulmonary visceral pleurae and do not communicate with the bronchial tree. (medscape.com)
- Pulmonary sequestration is a malformation comprised of dysplastic lung tissue without normal communication with the tracheobronchial tree and with an anomalous systemic arterial supply. (johnshopkins.edu)
- Pulmonary sequestration is classified into two types, intralobar and extralobar based on the location of the malformation and the venous drainage. (johnshopkins.edu)
- These lesions often show intense contrast enhancement and may even be associated with aberrant systemic arterial supply, resembling pulmonary sequestration.The treatment of choice for thoracic IMT is limited surgical resection, with corticosteroid therapy or radiation reserved for unresectable patients or patients with inadequate surgical margins. (elsevierpure.com)
- The aim of the study was to review the clinical characteristics of operated patients with respect to pulmonary sequestration and analyze diagnostic and therapeutic problems connected with this anomaly.Material and methods. (edu.pl)
- We performed a retrospective analysis of 23 patients operated on because of pulmonary sequestration between 1963 and 2004 in the Departments of Thoracic Surgery in Zakopane (10 patients) and Szczecin-Zdunowo (13 patients).Results. (edu.pl)
- Preoperatively, pulmonary sequestration was suspected in 5 patients. (edu.pl)
- In 5 patients, the pulmonary sequestration was supplied by more than one artery. (edu.pl)
- 1. Pulmonary sequestration in adults is difficult to diagnose before the operation, even with a detailed computer tomography examination. (edu.pl)
- Clements BS, Warner JO: Pulmonary sequestration and related congenital bronchopulmonary-vascular malformations: nomenclature and classification based on anatomical and embryological considerations. (edu.pl)
- Khalil KG, Kilman JW: Pulmonary sequestration. (edu.pl)
- Watine O, Mensier E, Delecluse P: Pulmonary sequestration treated by video-assisted thoracoscopic resection. (edu.pl)
- Congenital pulmonary malformations (CPM) comprise a group of anatomical abnormalities of the respiratory tree including congenital cystic malformations, bronchopulmonary sequestrations, bronchogenic cyst, bronchial atresia and congenital lobar emphysema.Socioeconomic, demographic, and hospital factors were determinants of survival of CPM. (ac.ir)
- Congenital pulmonary airway malformation (CPAM), formerly known as congenital cystic adenomatoid malformation (CCAM), is a congenital disorder of the lung similar to bronchopulmonary sequestration. (icd.codes)
- Indications for resection are wide ranging and include infection, cavitary lesions, bullous disease, bronchopulmonary sequestrations (BPSs), congenital lobar emphysema (CLE), cystic pulmonary adenomatoid malformations (CPAMs), and neoplasms. (abdominalkey.com)
- The differential diagnosis may include other lesions that are categorized as space-occupying, eg, congenital pulmonary airway malformation, bronchopulmonary sequestration, bronchogenic cyst, congenital diaphragmatic hernia, and Swyer-James-McLeod syndrome (unilateral hyperlucent lung syndrome) (2). (figshare.com)
Intralobar sequestration5
- When a fetus develops a cystic piece of nonfunctioning abnormal lung tissue either within a lung (intralobar sequestration) or next to it (extralobar- more common in boys) that is not connected to the body's airways, its known as bronchopulmonary sequestration. (nicklauschildrens.org)
- Intralobar sequestration in which the lesion is located within a normal lobe and lacks its own visceral pleura. (wikipedia.org)
- At thoracotomy after birth, an intralobar sequestration was confirmed. (medscape.com)
- Extralobar sequestration is less common than intralobar sequestration and usually has systemic venous drainage into the azygos system. (johnshopkins.edu)
- 2. Intralobar sequestration is much more common (87%) than extralobar and is often situated in the basal segments with comparable incidence on the right and left sides. (edu.pl)
Lesions1
- Going With the Flow: An Aid in Detecting and Differentiating Bronchopulmonary Sequestrations and Hybrid Lesions. (chop.edu)
Malformation2
- citation needed] Bronchopulmonary sequestration (BPS) is a rare congenital malformation of the lower respiratory tract. (wikipedia.org)
- When this area fails to clear after a course of appropriate medical therapy, the presence of a malformation, such as sequestration, should be considered, particularly if the lesion is localized to the posterior basal segment of the left lower lobe. (medscape.com)
Cystic1
- Because no communication with the bronchial tree occurs, sequestration appears to have loose, spongy tissue with numerous small cystic spaces containing clear, mucoid fluid. (medscape.com)
Abnormalities1
- Unlike extralobar sequestration, it is rarely associated with other developmental abnormalities. (wikipedia.org)
Lesion1
- The other type of lung lesion is called a bronchopulmonary sequestration, or BPS. (mottchildren.org)
Lower lobe3
- Two thirds of the time, the sequestration is located in the paravertebral gutter in the posterior segment of the left lower lobe. (wikipedia.org)
- If no communication between sequestration and normal lung tissue is present, radiography usually reveals a dense opacity in the posterior basal segment of the lower lobe. (medscape.com)
- In ELS, 80% of sequestrations lie between the lower lobe and the diaphragm. (medscape.com)
Congenital abnormality1
- Bronchopulmonary sequestration is surely a congenital abnormality defined as as well intralobar and even extraIobar along with returns on the inside chronic reduced breathing device tact microbe infections contributing tó bronchiectasis. (souzabianco.com.br)
Systemic1
- These attachments to the aorta remain to form the systemic arterial supply of the sequestration. (wikipedia.org)
Extrapulmonary2
- Extrapulmonary sequestration is completely enclosed in its own pleural sac. (wikipedia.org)
- Distinguishing an intrapulmonary sequestration from extrapulmonary sequestration is difficult using plain radiography. (medscape.com)
Intrapulmonary1
- Intrapulmonary sequestration occurs within the visceral pleura of normal lung tissue. (wikipedia.org)
Prenatally1
- Bronchopulmonary sequestration may be diagnosed prenatally and have no symptoms during the neonatal period. (nicklauschildrens.org)
Gastrointestinal1
- Extralobar sequestration may present with gastrointestinal symptoms i.e feeding difficulties. (nicklauschildrens.org)
Accessory lung2
- The most frequently supported theory of sequestration formation involves an accessory lung bud that develops from the ventral aspect of the primitive foregut. (wikipedia.org)
- Early embryologic development of the accessory lung bud results in formation of the sequestration within normal lung tissue. (wikipedia.org)
Aberrant1
- The sequestration (S) is linked by an aberrant vessel (arrows). (medscape.com)
Pleural1
- The sequestration is encased within the same pleural covering. (wikipedia.org)
Abdominal aorta2
- Both types of sequestration usually have arterial supply from the thoracic or abdominal aorta. (wikipedia.org)
- 73% of sequestrations develop blood vessels leading off the abdominal aorta, and 18% develop blood vessels leading off the thoracic aorta. (medscape.com)
Typically1
- A bronchopulmonary sequestration is typically removed surgically a short time after the baby is born. (nicklauschildrens.org)
Patients1
- Most patients with extralobar sequestration are diagnosed before the age of 10. (johnshopkins.edu)
Mass1
- We present an interesting and unusual case of extralobar sequestration which presented as a retroperitoneal mass in an asymptomatic adult. (johnshopkins.edu)
Diaphragm1
- We found 20 intralobar sequestrations and 3 extralobar sequestrations, which were situated above the diaphragm. (edu.pl)
Children1
- Telander RL, Lennox C, Sieber W. Sequestration of the lung in children. (medscape.com)
Malformation5
- ENGLISH ABSTRACT: BACKGROUND AND PURPOSE: Fetal cystic lung lesions, such as congenital cystic adenomatoid malformation of the lung (CCAM) and bronchopulmonary sequestration (BPS), were once considered rare and of poor prognosis. (uni-muenchen.de)
- It is widely believed that extralobar pulmonary sequestrations are a result of prenatal pulmonary malformation while intralobar pulmonary sequestrations can develop due to recurrent pulmonary infections in adolescents and young adults. (wikipedia.org)
- citation needed] Bronchopulmonary sequestration (BPS) is a rare congenital malformation of the lower respiratory tract. (wikipedia.org)
- Congenital pulmonary airway malformation (CPAM), bronchopulmonary sequestration and congenital lobar emphysema are the most common types of congenital lung lesions. (nationwidechildrens.org)
- Increased expression of this gene is associated with a distinct biologic subset of acute myeloid leukemia (AML) and the occurrence of bronchopulmonary sequestration (BPS) and congenital cystic adenomatoid malformation (CCAM) tissue. (nih.gov)
Dysplasia2
- His laboratory conducted research on how the lung's airspaces become fluid filled (mechanisms of pulmonary edema), how airspace fluid is cleared under both physiologic (fetal lung liquid at birth) and pathophysiologic (pulmonary edema) conditions and population-based studies to discover genetic influences on the development of bronchopulmonary dysplasia and the long term outcomes of neonatal lung disease. (stanford.edu)
- Infants may recover completely or develop chronic lung damage, resulting in bronchopulmonary dysplasia (BPD). (medscape.com)
Lung6
- A pulmonary sequestration is a medical condition wherein a piece of tissue that ultimately develops into lung tissue is not attached to the pulmonary arterial blood supply, as is the case in normally developing lung. (wikipedia.org)
- The most frequently supported theory of sequestration formation involves an accessory lung bud that develops from the ventral aspect of the primitive foregut. (wikipedia.org)
- Early embryologic development of the accessory lung bud results in formation of the sequestration within normal lung tissue. (wikipedia.org)
- Intrapulmonary sequestration occurs within the visceral pleura of normal lung tissue. (wikipedia.org)
- The most common location is in the posterior basal segment, and nearly two thirds of pulmonary sequestrations appear in the left lung. (wikipedia.org)
- Extralobar sequestration in which the mass is located outside the normal lung and has its own visceral pleuraThe blood supply of 75% of pulmonary sequestrations is derived from the thoracic or abdominal aorta. (wikipedia.org)
Intralobar4
- Intralobar sequestration in which the lesion is located within a normal lobe and lacks its own visceral pleura. (wikipedia.org)
- citation needed] The intralobar variety accounts for 75 percent of all sequestrations. (wikipedia.org)
- 3. A case of concomitant intralobar bronchopulmonary sequestration and situs inversus totalis. (nih.gov)
- 13. Intralobar sequestration with situs inversus totalis. (nih.gov)
CPAM1
- These cases comprised 34 congenital pulmonary airway malformations (CPAM), 15 pulmonary sequestrations (PS), and 20 hybrid lesions. (ox.ac.uk)
Anomalies1
- Pleural effusions can be isolated (primary hydrothorax, also called called chylothorax) or secondary to other conditions such as bronchopulmonary sequestrations (BPS), CDH, cardiac anomalies, fetal infections, metabolic disorders, chromosomal or syndromal disorders. (ontariofetalcentre.ca)
Extralobar2
- Unlike extralobar sequestration, it is rarely associated with other developmental abnormalities. (wikipedia.org)
- Extralobar bronchopulmonary sequestration complicated by Nocardia Asteroides infection: a case report. (kfsyscc.org)
Bronchiectasis1
- These include: Potentially fatal hemorrhage The creation of a left-right shunt, where blood flows in a shortcut through the feed off the aorta Chronic infection with diseases such as Bronchiectasis Tuberculosis Aspergillosis Bronchial carcinoid Bronchogenic squamous cell carcinoma There is still much debate to whether pulmonary sequestration is a congenital problem or acquired through recurrent pulmonary infection. (wikipedia.org)
Abnormal1
- CA19-9 could be generated by abnormal columnar epithelia in pulmonary sequestration tissues and was transported into circulation after alveoli damage. (biomedcentral.com)
Diseases1
- Ho Kaufman Mcalister Syndrome or bronchopulmonary sequestration are other congenital diseases. (whatdoesmean.net)
Complications1
- Failure to have a pulmonary sequestration removed can lead to a number of complications. (wikipedia.org)
Types1
- Both types of sequestration usually have arterial supply from the thoracic or abdominal aorta. (wikipedia.org)
Completely1
- Extrapulmonary sequestration is completely enclosed in its own pleural sac. (wikipedia.org)