Double Outlet Right Ventricle
Incomplete transposition of the great vessels in which both the AORTA and the PULMONARY ARTERY arise from the RIGHT VENTRICLE. The only outlet of the LEFT VENTRICLE is a large ventricular septal defect (VENTRICULAR SEPTAL DEFECTS or VSD). The various subtypes are classified by the location of the septal defect, such as subaortic, subpulmonary, or noncommitted.
Heart Septal Defects, Ventricular
Developmental abnormalities in any portion of the VENTRICULAR SEPTUM resulting in abnormal communications between the two lower chambers of the heart. Classification of ventricular septal defects is based on location of the communication, such as perimembranous, inlet, outlet (infundibular), central muscular, marginal muscular, or apical muscular defect.
Heart Defects, Congenital
Ventricular Septum
The muscular structure separating the right and the left lower chambers (HEART VENTRICLES) of the heart. The ventricular septum consists of a very small membranous portion just beneath the AORTIC VALVE, and a large thick muscular portion consisting of three sections including the inlet septum, the trabecular septum, and the outlet septum.
Transposition of Great Vessels
A congenital cardiovascular malformation in which the AORTA arises entirely from the RIGHT VENTRICLE, and the PULMONARY ARTERY arises from the LEFT VENTRICLE. Consequently, the pulmonary and the systemic circulations are parallel and not sequential, so that the venous return from the peripheral circulation is re-circulated by the right ventricle via aorta to the systemic circulation without being oxygenated in the lungs. This is a potentially lethal form of heart disease in newborns and infants.
Heart Septal Defects
Pulmonary Valve Stenosis
Tetralogy of Fallot
A combination of congenital heart defects consisting of four key features including VENTRICULAR SEPTAL DEFECTS; PULMONARY STENOSIS; RIGHT VENTRICULAR HYPERTROPHY; and a dextro-positioned AORTA. In this condition, blood from both ventricles (oxygen-rich and oxygen-poor) is pumped into the body often causing CYANOSIS.
Heart Ventricles
Evolution of risk factors influencing early mortality of the arterial switch operation. (1/36)
OBJECTIVES: The present study was undertaken to determine the independent risk factors for early mortality in the current era after arterial switch operation (ASO). BACKGROUND: Prior reports on factors affecting outcome of the ASO demonstrated that abnormal coronary arterial patterns were associated with increased risk of early mortality. As diagnostic, surgical and perioperative management techniques continue to evolve, the risk factors for the ASO may have changed. METHODS: All patients who underwent the ASO at Children's Hospital, Boston between January 1, 1992 and December 31, 1996 were included. Hospital charts, echocardiographic and cardiac catheterization data and operative reports of all patients were reviewed. Demographics and preoperative, intraoperative and postoperative variables were recorded. RESULTS: Of the 223 patients included in the study (median age at ASO = 6 days and median weight = 3.5 kg), 26 patients had aortic arch obstruction or interruption, 12 had Taussig-Bing anomaly, 12 had multiple ventricular septal defects, 8 had right ventricular hypoplasia and 6 were premature. There were 16 early deaths (7%), with 3 deaths in the 109 patients considered "low risk" (2.7%). Coronary artery pattern was not associated with an increased risk of death. Compared with usual coronary anatomy pattern, however, inverted coronary patterns and single right coronary patterns were associated with increased incidence of delayed sternal closure (p = 0.003) and longer duration of mechanical ventilation (p = 0.008). In a multivariate logistic regression model using only preoperative variables, aortic arch repair at a separate procedure before ASO and smaller birth weight were independent predictors of early mortality. In a second model that included both pre- and intraoperative variables, circulatory arrest time and right ventricular hypoplasia were independent predictors of early death. CONCLUSIONS: The ASO can be performed in the current era without excess early mortality related to uncommon coronary artery patterns. Aortic arch repair before ASO, right ventricular hypoplasia, lower birth weight and longer intraoperative support continue to be independent risk factors for early mortality after the ASO. (+info)Double-outlet right ventricle: an antenatal diagnostic dilemma. (2/36)
OBJECTIVE: The purpose of this study was to describe the antenatal ultrasonographic findings of fetuses with double-outlet right ventricle (DORV). DESIGN: The records were reviewed of all fetuses scanned in our ultrasound unit which were suspected of having DORV during a 6-year period ending in April 1996. A medical record search for all infants with a postnatal diagnosis of DORV was also undertaken to identify cases that were not detected antenatally. Records were examined to determine the accuracy of antenatal diagnosis and the reasons for diagnostic errors. Fetuses without follow-up were excluded. RESULTS: There were 20 fetuses with antenatally detected conotruncal defects that had DORV included in the differential diagnosis. Three fetuses were excluded, seven did not have DORV and ten were confirmed postnatally as having DORV. Two additional infants were found to have DORV from the medical record search, producing a total of 12 cases. Antenatal sonographic cardiac findings included malpositioned (overriding or transposed) great arteries (n = 11), ventricular septal defect (n = 11) and small pulmonary artery suggesting stenosis (n = 4). Confirmed postnatal cardiac findings that were missed antenatally included aortic coarctation (n = 2), right-sided aortic arch (n = 2) and pulmonary stenosis (n = 1). Seven of the 12 fetuses had extracardiac findings. Nine of the 12 fetuses tested had a normal karyotype. Eleven of the 12 infants were liveborn. Nine of these 11 survived the neonatal period and underwent surgical repair within the first year of life; two subsequently died. In total, seven fetuses survived and five did not. CONCLUSIONS: Most fetuses with DORV can be identified antenatally as having an abnormal heart. However, it is very difficult to distinguish this particular defect from other conotruncal abnormalities. (+info)Double outlet right ventricle with anterior and left-sided aorta and subpulmonary ventricular septal defect. (3/36)
Double outlet right ventricle (DORV) is a heterogeneous group of abnormal ventriculoarterial connections where, by definition, both great arteries (pulmonary artery and aorta) arise primarily from the morphologically right ventricle. This condition affects 1-1.5% of the patients with congenital heart diseases, with a frequency of 1 in each 10,000 live births. We report the case of an 18-day-old infant with DORV and extremely rare anatomical features, such as anterior and left-sided aorta and subpulmonary ventricular septal defect (VSD). In addition to the anatomic features, the role of the echocardiogram for guiding the diagnosis and the surgical therapy of this congenital heart disease are discussed. (+info)Antitachycardia burst pacing for pleomorphic reentrant ventricular tachycardias associated with non-coronary artery diseases: a morphology specific programming for ventricular tachycardias. (4/36)
To study the role of antitachycardia burst pacing in patients with reentrant pleomorphic ventricular tachycardia (VT) associated with non-coronary artery diseases, the efficacy of antitachycardia pacing and appropriate antitachycardia pacing cycle length were evaluated in each pleomorphic VT morphology of seven patients. Seven patients were included in this study. Clinically documented pleomorphic VTs were reproduced in an electrophysiologic study. For each VT, rapid ventricular pacing was attempted from the apex of the right ventricle at a cycle length which was 20 ms shorter than that of VT and repeated after a decrement of the cycle length in steps of 10 ms until the VT was terminated or accelerated. All 16 VTs could be entrained by the rapid pacing, and 13 of the 16 VTs (81%) were terminated, whereas pacing-induced acceleration was observed in the other 3 VTs of the 3 patients. VT cycle length (VTCL), block cycle length (BCL) which was defined as the longest VT interrupting paced cycle length, %BCL/VTCL and entrainment zone which was defined as VTCL minus BCL, varied in each VT morphology of each patient. In two patients, antitachycardia pacing was effective in all VT morphologies and the maximum difference of the %BCL/VTCL among the pleomorphic VTs was less than 10%. Thus, antitachycardia pacing seemed to be beneficial for these patients. In the other 5 patients, a difference of more than 10% in %BCL/VTCL was observed among the pleomorphic VT morphologies and/or at least one VT morphology showed pacing-induced acceleration. Compared to the 13 terminated VTs, three accelerated VTs had a wide entrainment zone [160 +/- 44 vs 90 +/- 48 ms, p < 0.04] and small %BCL/VTCL [61 +/- 6 vs 77 +/- 11%,p<0.03]. In pleomorphic VTs associated with non-coronary artery diseases, responses to rapid pacing was not uniform; VT might be terminable or accelerated even in the same patient. We need to pay close attention when programming antitachycardia pacing in patients with pleomorphic VT. (+info)Cardiovascular defects associated with abnormalities in midline development in the Loop-tail mouse mutant. (5/36)
Loop-tail (Lp) is a naturally occurring mouse mutant that develops severe neural tube defects. In this study, we describe complex cardiovascular defects in Lp homozygotes, which include double-outlet right ventricle, with obligatory perimembranous ventricular septal defects, and double-sided aortic arch, with associated abnormalities in the aortic arch arteries. Outflow tract and aortic arch defects are often related to abnormalities in the cardiac neural crest, but using molecular and anatomic markers, we show that neural crest migration is normal in Lp/Lp embryos. On the other hand, the heart fails to loop normally in Lp/Lp embryos, in association with incomplete axial rotation and reduced cervical flexion. As a consequence, the ventricular loop is shifted posteromedially relative to its position in wild-type embryos. This suggests that the observed cardiac alignment defects in the Lp mutant may be secondary to failure of neural tube closure and incomplete axial rotation. Double-sided aortic arch is a rare finding among mouse models. In humans, it is usually an isolated malformation, only rarely occurring in combination with other cardiac defects. We suggest that the double-sided arch arises as a primary defect in the Lp mutant, unrelated to the alignment defects, perhaps reflecting a role for the (as-yet-unknown) Lp gene in maintenance/regression of the aortic arch system. (+info)Echocardiographic characteristics and outcome of straddling mitral valve. (6/36)
OBJECTIVES: This study sought to characterize the echocardiographic features of straddling mitral valve (SMV) and to determine its surgical implications and midterm outcome in a large clinical cohort. BACKGROUND: Despite a relatively large body of literature on the postmortem anatomy of SMV, there is a paucity of information regarding its echocardiographic features, surgical implications and preoperative predictors of outcome. METHODS: A retrospective review identified 46 patients with SMV between 1982 and 1999 who underwent echocardiography and surgery and had follow-up data. A detailed review of the echocardiograms, surgical reports and all pertinent records was undertaken. RESULTS: Review of the echocardiograms revealed a widely varying anatomy among the study patients. However, four distinct groups with relatively uniform morphologic features could be distinguished on the basis of segmental analysis. Cardiac malposition associated with right ventricular hypoplasia, superior-inferior ventricles and criss-cross atrioventricular relations were common among patients with [S,D,L] (S = visceroatrial situs solitus, D = D-ventricular loop, L = L-malposition of the great arteries) (n = 6) and [S,L,D] (n = 5) segmental combinations but were rare among patients with [S,D,D] (n = 26) and [S,L,L] (n = 9) combinations. Surgical management consisted of a functional single-ventricle palliation in 38 patients (83%) and biventricular repair in 8 patients (17%). Overall mortality was 22%, but none of the seven patients who were operated on during the cohort's last five years (1994 to 1999) has died. By multivariate analysis, noncommitted ventricular septal defect was the strongest independent predictor of death (relative risk = 10.2), followed by multiple ventricular septal defects (relative risk = 4.7). CONCLUSIONS: This study demonstrates that echocardiography provides detailed noninvasive imaging of the complex anatomic features of SMV and its associated anomalies. Anatomic classification based on segmental analysis allows the distinction of four groups with more uniform morphologic features. Although a biventricular approach is feasible in selected patients, a functional univentricular palliation is indicated in those with major straddling and markedly hypoplastic ventricles. (+info)CFC1 mutations in patients with transposition of the great arteries and double-outlet right ventricle. (7/36)
Recent investigations identified heterozygous CFC1 mutations in subjects with heterotaxy syndrome, all of whom had congenital cardiac malformations, including malposition of the great arteries. We hypothesized that a subset of patients with similar types of congenital heart disease---namely, transposition of the great arteries and double-outlet right ventricle, in the absence of laterality defects---would also have CFC1 mutations. Our analysis of the CFC1 gene in patients with these cardiac disorders identified two disease-related mutations in 86 patients. The present study identifies the first autosomal single-gene defect for these cardiac malformations and indicates that some cases of transposition of the great arteries and double-outlet right ventricle can share a common genetic etiology with heterotaxy syndrome. In addition, these results demonstrate that the molecular pathway involving CFC1 plays a critical role in normal and abnormal cardiovascular development. (+info)Long-term predictors of aortic root dilation and aortic regurgitation after arterial switch operation. (8/36)
BACKGROUND: Neo-aortic root dilation (ARD) and neo-aortic regurgitation (AR) may be progressive after arterial switch operation (ASO) for d-loop transposition of the great arteries (dTGA). We sought to identify predictors of ARD and AR after ASO. METHODS AND RESULTS: 335 patients were identified who underwent ASO for dTGA with intact ventricular septum or ventricular septal defect (VSD), including double-outlet right ventricle (DORV), before 2001 with at least 1 postoperative echocardiogram at our institution, at least 1 year after ASO, and no previous atrial switch procedure (median follow-up of 5.0 years). Probability of freedom from ARD was 97%, 92%, 82%, and 51%, from at least moderate AR was 98%, 97%, 96%, and 93%, and from neo-aortic valve or root surgery was 100%, 100%, 99%, and 95%, at 1, 2, 5, and 10 years, respectively. For patients in whom ARD developed, progressive dilation was not observed during late follow-up. By Kaplan-Meier method, independent predictors of ARD, with neo-aortic root z-score of > or =3.0, were previous pulmonary artery band (PAB) (P=0.002, hazard ratio [HR]=2.4) and later time period when ASO was performed (P<0.002, HR=19.0). Risk factor for at least moderate AR was age > or =1 year at ASO (P=0.002, HR=5.8), which was closely related to VSD repair at ASO (P<0.001) and previous PAB. CONCLUSIONS: Significant ARD and AR continue to develop over time after ASO, but ARD does not tend to be progressive during late follow-up. Previous PAB was a significant risk factor for ARD. Older age at time of ASO, presence of VSD, and previous PAB were risk factors for AR. (+info)Double Outlet Right Ventricle (DORV) is a congenital heart defect where both great vessels, the aorta and pulmonary artery, arise predominantly or entirely from the right ventricle, with various forms of ventricular septal defect determining the pathways for blood flow between the ventricles.
Double outlet right ventricle (DORV) is a congenital heart defect in which both great vessels (the aorta and the pulmonary artery) arise from the right ventricle. In a normal heart, the aorta arises from the left ventricle and the pulmonary artery arises from the right ventricle.
In DORV, there is a communication between the two ventricles (a ventricular septal defect), which allows oxygen-rich blood to mix with oxygen-poor blood. The location of this ventricular septal defect and the relationship of the great vessels to each other determine the physiology and the clinical manifestations of DORV.
DORV is a complex congenital heart defect that can range from mild to severe, and it often requires surgical intervention to improve blood flow and oxygenation. The prognosis for individuals with DORV depends on various factors, including the specific type of DORV, associated cardiac anomalies, and the timing and success of treatment.
A heart septal defect known as ventricular septal defect is a congenital condition characterized by an abnormal opening or hole in the interventricular septum, causing blood to flow between the left and right ventricles and leading to various cardiac complications.
A ventricular septal defect (VSD) is a type of congenital heart defect that involves a hole in the wall separating the two lower chambers of the heart, the ventricles. This defect allows oxygenated blood from the left ventricle to mix with deoxygenated blood in the right ventricle, leading to inefficient oxygenation of the body's tissues. The size and location of the hole can vary, and symptoms may range from none to severe, depending on the size of the defect and the amount of blood that is able to shunt between the ventricles. Small VSDs may close on their own over time, while larger defects usually require medical intervention, such as medication or surgery, to prevent complications like pulmonary hypertension and heart failure.
Angiocardiography is a medical procedure that uses real-time X-ray imaging and the injection of a contrast agent to visualize the heart and its blood vessels, assisting in the diagnosis and treatment of various cardiovascular conditions.
Angiocardiography is a medical procedure used to examine the heart and blood vessels, particularly the chambers of the heart and the valves between them. It involves injecting a contrast agent into the bloodstream and taking X-ray images as the agent flows through the heart. This allows doctors to visualize any abnormalities such as blockages, narrowing, or leakage in the heart valves or blood vessels.
There are different types of angiocardiography, including:
* Left heart catheterization (LHC): A thin tube called a catheter is inserted into a vein in the arm or groin and threaded through to the left side of the heart to measure pressure and oxygen levels.
* Right heart catheterization (RHC): Similar to LHC, but the catheter is threaded through to the right side of the heart to measure pressure and oxygen levels there.
* Selective angiocardiography: A catheter is used to inject the contrast agent into specific blood vessels or chambers of the heart to get a more detailed view.
Angiocardiography can help diagnose and evaluate various heart conditions, including congenital heart defects, coronary artery disease, cardiomyopathy, and valvular heart disease. It is an invasive procedure that carries some risks, such as bleeding, infection, and damage to blood vessels or heart tissue. However, it can provide valuable information for diagnosing and treating heart conditions.
'Heart Defects, Congenital' are structural abnormalities of the heart or great vessels present at birth, which can affect cardiac blood flow, causing various clinical manifestations and complications.
Congenital heart defects (CHDs) are structural abnormalities in the heart that are present at birth. They can affect any part of the heart's structure, including the walls of the heart, the valves inside the heart, and the major blood vessels that lead to and from the heart.
Congenital heart defects can range from mild to severe and can cause various symptoms depending on the type and severity of the defect. Some common symptoms of CHDs include cyanosis (a bluish tint to the skin, lips, and fingernails), shortness of breath, fatigue, poor feeding, and slow growth in infants and children.
There are many different types of congenital heart defects, including:
1. Septal defects: These are holes in the walls that separate the four chambers of the heart. The two most common septal defects are atrial septal defect (ASD) and ventricular septal defect (VSD).
2. Valve abnormalities: These include narrowed or leaky valves, which can affect blood flow through the heart.
3. Obstruction defects: These occur when blood flow is blocked or restricted due to narrowing or absence of a part of the heart's structure. Examples include pulmonary stenosis and coarctation of the aorta.
4. Cyanotic heart defects: These cause a lack of oxygen in the blood, leading to cyanosis. Examples include tetralogy of Fallot and transposition of the great arteries.
The causes of congenital heart defects are not fully understood, but genetic factors and environmental influences during pregnancy may play a role. Some CHDs can be detected before birth through prenatal testing, while others may not be diagnosed until after birth or later in childhood. Treatment for CHDs may include medication, surgery, or other interventions to improve blood flow and oxygenation of the body's tissues.
The ventricular septum is the thick, muscular wall that divides the left and right ventricles within the heart, primarily functioning to maintain the separate blood flow circuits of pulmonary and systemic circulations.
The ventricular septum is the thick, muscular wall that separates the left and right ventricles, which are the lower chambers of the heart. Its main function is to prevent the oxygen-rich blood in the left ventricle from mixing with the oxygen-poor blood in the right ventricle.
A congenital heart defect called a ventricular septal defect (VSD) can occur when there is an abnormal opening or hole in the ventricular septum, allowing blood to flow between the two ventricles. This can result in various symptoms and complications, depending on the size of the defect and the amount of blood that passes through it. VSDs are typically diagnosed and treated by pediatric cardiologists or cardiac surgeons.
Transposition of the Great Vessels is a congenital heart defect where the aorta and pulmonary artery are abnormally positioned, causing deoxygenated blood to flow back into the systemic circulation instead of going to the lungs for oxygenation.
Transposition of the Great Vessels is a congenital heart defect in which the two main vessels that carry blood from the heart to the rest of the body are switched in position. Normally, the aorta arises from the left ventricle and carries oxygenated blood to the body, while the pulmonary artery arises from the right ventricle and carries deoxygenated blood to the lungs. In transposition of the great vessels, the aorta arises from the right ventricle and the pulmonary artery arises from the left ventricle. This results in oxygen-poor blood being pumped to the body and oxygen-rich blood being recirculated back to the lungs, which can lead to serious health problems and is often fatal if not corrected through surgery soon after birth.
A heart septal defect is a congenital cardiac anomaly characterized by an abnormal opening or absence in the interatrial or interventricular septum, resulting in abnormal communication between the heart's chambers and leading to various clinical manifestations depending on the size, location, and hemodynamic impact of the defect.
A heart septal defect is a type of congenital heart defect, which means it is present at birth. It involves an abnormal opening in the septum, the wall that separates the two sides of the heart. This opening allows oxygen-rich blood to leak into the oxygen-poor blood chambers in the heart.
There are several types of heart septal defects, including:
1. Atrial Septal Defect (ASD): A hole in the atrial septum, the wall between the two upper chambers of the heart (the right and left atria).
2. Ventricular Septal Defect (VSD): A hole in the ventricular septum, the wall between the two lower chambers of the heart (the right and left ventricles).
3. Atrioventricular Septal Defect (AVSD): A combination of an ASD and a VSD, often accompanied by malformation of the mitral and/or tricuspid valves.
The severity of a heart septal defect depends on the size of the opening and its location in the septum. Small defects may cause no symptoms and may close on their own over time. Larger defects can lead to complications, such as heart failure, pulmonary hypertension, or infective endocarditis, and may require medical or surgical intervention.
Pulmonary Valve Stenosis is a cardiac condition characterized by the narrowing or stiffening of the pulmonary valve opening, causing obstruction to blood flow from the right ventricle to the pulmonary artery, often leading to right heart failure if left untreated.
Pulmonary Valve Stenosis is a cardiac condition where the pulmonary valve, located between the right ventricle and the pulmonary artery, has a narrowed opening. This stenosis (narrowing) can cause obstruction of blood flow from the right ventricle to the lungs. The narrowing can be caused by a fusion of the valve leaflets, thickened or calcified valve leaflets, or rarely, a dysplastic valve.
The severity of Pulmonary Valve Stenosis is classified based on the gradient pressure across the valve, which is measured during an echocardiogram. A mild stenosis has a gradient of less than 30 mmHg, moderate stenosis has a gradient between 30-59 mmHg, and severe stenosis has a gradient of 60 mmHg or higher.
Mild Pulmonary Valve Stenosis may not require treatment, while more severe cases may need to be treated with balloon valvuloplasty or surgical valve replacement. If left untreated, Pulmonary Valve Stenosis can lead to right ventricular hypertrophy, heart failure, and other complications.
Tetralogy of Fallot is a congenital heart defect characterized by the presence of four cardiac anomalies: ventricular septal defect, pulmonary stenosis, overriding aorta, and right ventricular hypertrophy.
Tetralogy of Fallot is a congenital heart defect that consists of four components: ventricular septal defect (a hole between the lower chambers of the heart), pulmonary stenosis (narrowing of the pulmonary valve and outflow tract), overriding aorta (the aorta lies directly over the ventricular septal defect), and right ventricular hypertrophy (thickening of the right ventricular muscle). This condition results in insufficient oxygenation of the blood, leading to cyanosis (bluish discoloration of the skin and mucous membranes) and other symptoms such as shortness of breath, fatigue, and poor growth. Treatment typically involves surgical repair, which is usually performed during infancy or early childhood.
The heart ventricles are the two lower chambers of the heart that receive blood from the atria and pump it to the lungs or the body through the pulmonary and systemic circulatory systems, respectively.
The heart ventricles are the two lower chambers of the heart that receive blood from the atria and pump it to the lungs or the rest of the body. The right ventricle pumps deoxygenated blood to the lungs, while the left ventricle pumps oxygenated blood to the rest of the body. Both ventricles have thick, muscular walls to generate the pressure necessary to pump blood through the circulatory system.
The heart is a muscular organ that functions as a pump to circulate blood throughout the body, receiving deoxygenated blood from the systemic circulation through the venous system and pumping it to the lungs for reoxygenation via the pulmonary circulation, before receiving the oxygenated blood back from the lungs and propelling it into the systemic circulation.
In medical terms, the heart is a muscular organ located in the thoracic cavity that functions as a pump to circulate blood throughout the body. It's responsible for delivering oxygen and nutrients to the tissues and removing carbon dioxide and other wastes. The human heart is divided into four chambers: two atria on the top and two ventricles on the bottom. The right side of the heart receives deoxygenated blood from the body and pumps it to the lungs, while the left side receives oxygenated blood from the lungs and pumps it out to the rest of the body. The heart's rhythmic contractions and relaxations are regulated by a complex electrical conduction system.
A newborn infant is a baby within the first 28 days of life, from birth to 1 month old, regardless of gestational age, birthweight, or status at birth. (Source: American Academy of Pediatrics & World Health Organization)
A newborn infant is a baby who is within the first 28 days of life. This period is also referred to as the neonatal period. Newborns require specialized care and attention due to their immature bodily systems and increased vulnerability to various health issues. They are closely monitored for signs of well-being, growth, and development during this critical time.
Gastric outlet obstruction is a condition characterized by the narrowing or blockage of the pyloric channel, causing partial or complete impediment to the passage of gastric contents into the duodenum.
Gastric outlet obstruction (GOO) is a medical condition that refers to the blockage of the passage from the stomach to the small intestine, also known as the pylorus. This blockage can be caused by various factors, including tumors, scar tissue, or gallstones. As a result, food and digestive enzymes cannot pass through the pylorus into the small intestine, leading to symptoms such as vomiting, abdominal pain, bloating, and weight loss. In severe cases, GOO can lead to malnutrition, dehydration, and other complications if left untreated. Treatment options for GOO depend on the underlying cause of the obstruction and may include medication, endoscopic procedures, or surgery.
Double outlet right ventricle
... (DORV) is a form of congenital heart disease where both of the great arteries connect (in whole ... Obler D, Juraszek AL, Smoot LB, Natowicz MR (August 2008). "Double outlet right ventricle: aetiologies and associations". J. ... blood from both ventricles is substantially mixed in the RV, yielding physiology that resembles a large VSD but again, if there ... in terms of altering the normal flow of blood from the RV and left ventricle (LV) to the aorta and pulmonary artery. For ...
List of OMIM disorder codes
DAX1 Double outlet right ventricle; 217095; CFC1 Double outlet right ventricle; 217095; GDF1 Dowling-Degos disease; 179850; ...
Helen B. Taussig
This is the second most common type of double-outlet right ventricle (DORV), a set of rare congenital heart conditions in which ... "Double outlet right ventricle : MedlinePlus Medical Encyclopedia". medlineplus.gov. Retrieved 2020-03-22. Callahan, Clara A. ( ... Taussig, Helen B.; Meserve, Faith L. (1925-03-01). "Rhythmic Contractions in Isolated Strips of Mammalian Ventricle". American ... instead is connected to the right ventricle and supplies oxygen-poor blood to the body. Several alternative methods for ...
B-cell activating factor
"Double outlet right ventricle and left-sided aorta. A previously undescribed association with cor triatriatum and double right ...
Crisscross heart
Taksande AM (April 2013). "Echocardiographic recognition of a criss-cross heart with double outlet right ventricle". Images in ... Angelini P (2010). "Left ventricle on top versus right ventricle on top in superoinferior ventricles: what are we talking about ... In an anatomically correct heart the atria are smaller than the ventricles. The ventricles include more muscle in order to push ... In opposition, when the left atrium and right atrium are relaxed the left ventricle and right ventricle contract pushing blood ...
CFC1
"CFC1 mutations in patients with transposition of the great arteries and double-outlet right ventricle". Am. J. Hum. Genet. 70 ( ...
Cardiac neural crest
These anomalies include persistent truncus arteriosus (PTA), double outlet right ventricle (DORV), tetralogy of Fallot and ... transposition of the great vessels and double outlet right ventricle. Overriding aorta is caused by the abnormal looping during ... The cardiac outflow tract is a temporary structure in the developing embryo that connects the ventricles with the aortic sac. ... Other outcomes of aortic arch artery anomalies includes a double aortic arch, variable absence of the carotid arteries and left ...
MYL4
Altered ALC-1 expression is also altered in other congenital heart diseases, Double outlet right ventricle and infundibular ... A developmental and anatomical study of heavy and light chain subunits in the atrium and ventricle". Circulation Research. 58 ( ... ALC-1 expression in cardiac ventricles decreases in early postnatal development, but is highly expressed in atria throughout ... Moreover, in patients with aortic stenosis or aortic insufficiency, ALC-1 expression in left ventricles was elevated, and ...
Pentalogy of Cantrell
Others include atrial septal defect, cardiac diverticulum, pulmonic stenosis, double outlet right ventricle, tetralogy of ...
Taussig-Bing syndrome
... is a cyanotic congenital heart defect in which the patient has both double outlet right ventricle (DORV) ... flows out to the aorta and blood from the right ventricle (RV) flows out to the pulmonary artery, both aorta and pulmonary ... and subpulmonic ventricular septal defect (VSD). In DORV, instead of the normal situation where blood from the left ventricle ( ...
Stanley John
... and Double Outlet Right Ventricle (DORV) in India. He assisted in performing the first open heart surgery in India while ...
Bidirectional Glenn procedure
... double-inlet left ventricle and double-outlet right ventricle.[1] The natural history of congenital univentricular cardiac ... In a single-ventricle heart, the sole functioning ventricle must pump blood to both the lungs and the organ systems. As a ... The aim of the bidirectional Glenn shunt is to improve oxygenation and reduce the load on the single functioning ventricle ... The Glenn procedure is typically performed at 4 to 6 months of age for infants born with congenital single ventricle defects. ...
Rastelli procedure
... or double outlet right ventricle (DORV); and Ventricular septal defect (VSD); and Right ventricular outflow tract obstruction ( ... and involves using a pulmonary or aortic homograft conduit to relieve pulmonary obstruction in double outlet right ventricle ... From the right ventricle to the pulmonary bifurcation, a synthetic conduit and a valve are constructed, which lets oxygen ... Oxygenated blood is directed from the left ventricle to the aorta using a Gore-Tex patch. The VSD is also sealed with the patch ...
Cardiology
Double outlet right ventricle (DORV) is when both great arteries, the pulmonary artery and the aorta, are connected to the ... Tetralogy of Fallot, pulmonary atresia, double outlet right ventricle, transposition of the great arteries, persistent truncus ... Switching the left ventricle to be the systemic ventricle and the right ventricle to pump blood into the pulmonary artery can ... One way it can be cured is by a VSD closure and placing conduits to restart the blood flow between the left ventricle and the ...
Single ventricle
... with functional left ventricle: Pulmonal atresia Tricuspidal atresia Double inlet left ventricle Double outlet ... Hypoplastic left heart syndrome Double inlet right ventricle Double outlet right ventricle Single ventricle heterotaxy syndrome ... The single functional ventricle could be morphologically right or left with the second ventricle usually hypoplastic and/or ... left ventricle Single ventricle with functional right ventricle: ... Single ventricle is a rare congenital heart defect, which ...
Ectopia cordis
... defects Atrial septal defect Ventricular septal defect Tetralogy of Fallot Tricuspid atresia Double outlet right ventricle Non- ...
List of circulatory system conditions
Dextro-Transposition of the great arteries Double aortic arch Double inlet left ventricle Double outlet right ventricle ...
Dextrocardia
... such as double outlet right ventricle, endocardial cushion defect and pulmonary stenosis). Certain cardiovascular and pulmonary ... Right sided structures such as right atrium, right ventricle and tricuspid valve are oriented posteriorly in dextrocardia situs ...
Congenital heart defect
Dextrocardia Double inlet left ventricle (DILV) Double outlet right ventricle (DORV) Ebstein's anomaly Early Repolarization ... Hypoplasia can affect the heart, typically resulting in the underdevelopment of the right ventricle or the left ventricle. This ... From days 23 through 28, the heart tube folds and twists, with the future ventricles moving left of center (the ultimate ... Double aortic arch, aberrant subclavian artery, and other malformations of the great arteries Interrupted aortic arch (IAA) ...
List of fetal abnormalities
... twins Cystic hygroma Dandy-Walker malformation Diaphragmatic hernia Diastrophic dysplasia Double outlet right ventricle ...
3C syndrome
... double outlet right ventricle, transposition of the great vessels, and hypoplastic left heart syndrome. Aortic stenosis and ... Besides the cerebellar hypoplasia, cysts are commonly found in the posterior cranial fossa, the ventricles and the cisterna ... and enlargement of the cisterna magna and fourth ventricle of the brain. Animal models of 3C syndrome have not been created; ...
Cor triatriatum
... double outlet right ventricle, coarctation of the aorta, partial anomalous pulmonary venous connection, persistent left ...
Hybrid cardiac surgery
... such as double-outlet right ventricle, or transposition of the great arteries, acute turns or kinks in the pulmonary arteries ... "Single-ventricle palliation for high-risk neonates: The emergence of an alternative hybrid stage I strategy". The Journal of ...
Pulmonary atresia
Tricuspid atresia Tetralogy of Fallot Double outlet right ventricle In terms of the cause of pulmonary atresia, there is ... The type of surgery recommended depends on the size of the right ventricle and the pulmonary artery, if the right ventricle is ... The pulmonary valve is located on the right side of the heart between the right ventricle and pulmonary artery. In a normal ... When this second opening does not exist, very little blood goes to the right ventricle, which is what causes it to be ...
Ventricular septal defect
... a double outlet right ventricle with one. A ventricular septal defect arises when the superior part of the interventricular ... The right ventricle pumps blood to the lungs to get oxygen, while the left ventricle pumps blood to the rest of the body to ... The murmur depends on the abnormal flow of blood from the left ventricle, through the VSD, to the right ventricle. If there is ... The defect allows oxygen-rich blood from the left ventricle to mix with oxygen-poor blood in the right ventricle. Most cases do ...
List of MeSH codes (C16)
... double outlet right ventricle MeSH C16.131.240.400.920 - tricuspid atresia MeSH C16.131.240.400.929 - truncus arteriosus, ...
List of diseases (D)
Double cortex Double discordia Double fingernail of fifth finger Double outlet left ventricle Double outlet right ventricle ... Double tachycardia induced by catecholamines Double uterus-hemivagina-renal agenesis Down syndrome Doxorubicin-induced ...
ZFPM2
... double outlet right ventricle, transposition of the great arteries, and interrupted aortic arch. Sporadic cases of Tetralogy of ...
NAA15
... double outlet right ventricle, hypoplastic RV, D-transposition of the great arteries, pulmonic stenosis) and hydronephrosis, ...
List of MeSH codes (C14)
... double outlet right ventricle MeSH C14.240.400.920 - tricuspid atresia MeSH C14.240.400.929 - truncus arteriosus, persistent ... double outlet right ventricle MeSH C14.280.400.920 - tricuspid atresia MeSH C14.280.400.929 - truncus arteriosus, persistent ...
Double outlet right ventricle - Wikipedia
Double outlet right ventricle (DORV) is a form of congenital heart disease where both of the great arteries connect (in whole ... Obler D, Juraszek AL, Smoot LB, Natowicz MR (August 2008). "Double outlet right ventricle: aetiologies and associations". J. ... blood from both ventricles is substantially mixed in the RV, yielding physiology that resembles a large VSD but again, if there ... in terms of altering the normal flow of blood from the RV and left ventricle (LV) to the aorta and pulmonary artery. For ...
Double Outlet Right Ventricle With Transposition: Background, Pathophysiology, Etiology
... arise entirely or predominantly from the right ventricle (RV). The only outlet from the left ventricle (LV) is a ventricular ... Double outlet right ventricle (DORV), as depicted in the image below, is a type of ventriculoarterial connection in which both ... encoded search term (Double Outlet Right Ventricle With Transposition) and Double Outlet Right Ventricle With Transposition ... hypertensive left ventricle and double outlet right ventricle: case report and literature review. Pediatr Cardiol. 2019 Jan. 40 ...
Double Outlet Right Ventricle Surgery Workup: Approach Considerations, Imaging Studies
The anatomic dysmorphology of double outlet right ventricle can vary from that of tetralog... ... The term double outlet right ventricle (DORV) refers to a heterogeneous series of associated cardiac anomalies that involve the ... right ventricular outflow tract in which both of the great arteries arise entirely or predominantly from the right ventricle. ... encoded search term (Double Outlet Right Ventricle Surgery) and Double Outlet Right Ventricle Surgery What to Read Next on ...
Double-outlet right ventricle | Sparrow
OverviewDouble-outlet right ventricle is a heart condition present at birth. That means its a congenital heart defect. In this ... Some babies with double-outlet right ventricle need heart repair surgery within the first few days of birth. Others may have ... Double-outlet right ventricle is a heart condition present at birth. That means its a congenital heart defect. In this ... In babies with double-outlet right ventricle, both the aorta and the pulmonary artery connect partially or completely to the ...
LHM Kidz - Double Outlet Right Ventricle - Little Hearts Matter
Double Outlet Right Ventricle. If you have DORV you have one big ventricle instead of two and blood travels from the heart in ... LHM Kidz - Double Outlet Right Ventricle. *Home / *LHM Kidz - Double Outlet Right Ventricle ... ️ We are the only national UK charity offering specialised support to anyone affected by the diagnosis of single ventricle ... Double Outlet Right Ventricle ...
Double Outlet Right Ventricle
Learn how our Fetal Heart specialists monitor double outlet right ventricle during your pregnancy. ... Double outlet right ventricle (DORV) is a congenital heart defect that occurs when the aorta and the main pulmonary artery both ... connect to the right ventricle instead the aorta connecting to the left ventricle. Other heart conditions can occur with DORV, ...
Double outlet right ventricle with pulmonary stenosis - ULTRASOUNDPAEDIA
double outlet right ventricle
Double outlet right ventricle, Double outlet right ventricle (disorder), Double outlet right ventricle NOS (disorder), Double ... outlet right ventricle with subpulmonary ventricular septal defect, Double outlet right ventricle, unspecified (disorder), ... DOID:6406 - double outlet right ventricle. Disease Ontology Definition:n_a Synonyms: Dextrotransposition of aorta, ...
Double Outlet Right Ventricle - Pediatrics - MSD Manual Professional Edition
Double Outlet Right Ventricle - Etiology, pathophysiology, symptoms, signs, diagnosis & prognosis from the MSD Manuals - ... Major Variants of Double Outlet Right Ventricle (DORV). AO = aorta; LA = left atrium; LV = left ventricle; PA = pulmonary ... In double outlet right ventricle (DORV), both the aorta and pulmonary valve connect to the right ventricle. A ventricular ... In double outlet right ventricle (DORV), both the aorta and pulmonary valve connect to the right ventricle. ...
Anesthetic management for cesarean section in a patient with uncorrected double-outlet right ventricle | SpringerPlus | Full...
Double-outlet right ventricle is a seldom disease and pregnancy with uncorrected double-outlet right ventricle ... Echocardiography indicated that she had congenital heart disease of double-outlet right ventricle. She hadnt received any ... continuous phenylephrine infusion is a preferable choice for parturient women with uncorrected double-outlet right ventricle ... Most of the aorta arises from the right ventricle, the volume of venous blood was injected from the right ventricle into the ...
Double Outlet Right Ventricle Surgery: Background, History of the Procedure, Problem
The anatomic dysmorphology of double outlet right ventricle can vary from that of tetralog... ... The term double outlet right ventricle (DORV) refers to a heterogeneous series of associated cardiac anomalies that involve the ... right ventricular outflow tract in which both of the great arteries arise entirely or predominantly from the right ventricle. ... double outlet right ventricle with subpulmonary VSD, double outlet right ventricle with doubly committed VSD, and double outlet ...
What is Double Outlet Right Ventricle ? Find Treatment Now | Anavara
The best treatments available worldwide for Double Outlet Right Ventricle. Contact Anavara today for your free quote! ... Double Outlet Right Ventricle. Home / Double Outlet Right Ventricle. In double-outlet right ventricle (DORV) a heart condition ... Double Outlet Right Ventricle. In double-outlet right ventricle (DORV) a heart condition present at birth (congenital) the main ... In people with double-outlet right ventricle, there is also a hole between the lower heart chambers (ventricles), called a ...
ESC 365 - Brain Abscess in an Adult with Unrepaired Double-Outlet Right Ventricle with Transposition of Great Arteries and...
Inpatient Hospitalization Costs Associated with Birth Defects Among Persons Aged 65 Years - United States, 2019 | MMWR
Double outlet. right ventricle. 805. 111,159. 1,640. 127,862. 1,110. 77,471. 490. 78,043. 315. 77,532. 4,360. 102,714. ... double outlet right ventricle (Q20.1), transposition of the great arteries (Q20.3), single ventricle (Q20.4), tetralogy of ... Single ventricle. 340. 155,126. 1,010. 166,406. 750. 66,991. 485. 61,920. 515. 42,193. 3,100. 104,135. ...
Double Outlet Right Ventricle | Fetology: Diagnosis and Management of the Fetal Patient, 2e | AccessObGyn | McGraw Hill Medical
"Double Outlet Right Ventricle." Fetology: Diagnosis and Management of the Fetal Patient, Second Edition Bianchi DW, ... Double Outlet Right Ventricle. In: Bianchi DW, Crombleholme TM, DAlton ME, Malone FD. Bianchi D.W., & Crombleholme T.M., & ... Double outlet right ventricle. Bianchi DW, Crombleholme TM, DAlton ME, Malone FD. Bianchi D.W., & Crombleholme T.M., & DAlton ... Double outlet right ventricle (DORV) refers to a congenital cardiac malformation in which most of the pulmonary artery and the ...
Double outlet right ventricle with subpulmonary ventricular septal defect without pulmonary stenosis (Concept Id: C1956413)
-...
... ventricles) of the heart), that is considered to be closely related to the pulmonary origin. There is not associated pulmonary ... A double outlet right ventricle with a ventricular spetal defect (a hole between the two bottom chambers ( ... Double outlet right ventricle*Double outlet right ventricle with subpulmonary ventricular septal defect without pulmonary ... Double outlet right ventricle with subpulmonary ventricular septal defect withou... Double outlet right ventricle with ...
Congenital Heart Disease | Congenital Heart Defects | MedlinePlus
Borderline left ventricles in prenatally diagnosed atrioventricular septal defect or double outlet right ventricle:...
Borderline left ventricles in prenatally diagnosed atrioventricular septal defect or double outlet right ventricle: ... BACKGROUND: Atrioventricular septal defect (AVSD) and double outlet right ventricle (DORV) with normally related great arteries ... The outcome of cases with a borderline small left ventricle (bLV) is unclear. The purpose of the study was to retrospectively ... Fetal echocardiographic parameters comparing BV repair versus single ventricle (SV) palliation were obtained, including the ...
Surgical treatment of subaortic stenosis after biventricular repair of double-outlet right ventricle Emre Belli, MD, Alain...
1 Surgical treatment of subaortic stenosis after biventricular repair of double-outlet right ventricle Emre Belli, MD, Alain ... Repair of Atrioventricular Septal Defect Associated With Tetralogy of Fallot or Double- Outlet Right Ventricle: 30 Years of ... Surgical treatment of subaortic stenosis after biventricular repair of double-outlet right ventricle Emre Belli, MD, Alain ... Download ppt "Surgical treatment of subaortic stenosis after biventricular repair of double-outlet right ventricle Emre Belli, ...
Two-dimensional echocardiographic diagnosis of double outlet left ventricle with subaortic ventricular septal defect, pulmonary...
Double outlet left ventricle (DOLV) is a rare congenital cardiac malformation in which both the pulmonary artery and the aorta ... Two-dimensional echocardiographic diagnosis of double outlet left ventricle with subaortic ventricular septal defect, pulmonary ... We describe a case of DOLV with situs solitus, d-loop ventricles, d-malposition of the great arteries (S, D, D), severe ... morphologic variations of this malformation have been described but to the our knowledge DOLV with a hypoplastic left ventricle ...
MedlinePlus - Search Results for: Coarctation of aorta
The Fetal Care Center of Southern California - Fetal Care & Diagnostic Center
Diagnosis of severe congenital heart defects in Norway 2016 | Tidsskrift for Den norske legeforening
Dr. Luis Scott, MD, Clinical Cardiac Electrophysiologist - Phoenix, AZ | Sharecare
A Helping Hand for Children with Congenital Heart Disease | Maxim Healthcare Services
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Single ventricleDORVConnected to the right ventrInjected from the right ventricleTranspositionTetralogyOutflow tractVentricular SeptumAnatomicPredominantlyGreat arteriesCardiacDefectsLeftAriseTaussig-BingRight atriumLethalityEndocardialDiagnosis of doubleDefinitionOccursBlood vesselIncidenceBabiesChambersFallotSurgeryDisorders
Single ventricle4
- Welcome to Little Hearts Matter ❤️ We are the only national UK charity offering specialised support to anyone affected by the diagnosis of single ventricle heart condition. (lhm.org.uk)
- Fetal echocardiographic parameters comparing BV repair versus single ventricle (SV) palliation were obtained, including the presence or absence of an apex-forming bLV was recorded. (mcmaster.ca)
- In format the book appears similar to a large collection of case reports covering all types of congenital heart disease, including complex lesions such as single ventricle and atrial isomerism. (stanford.edu)
- The Single Ventricle Home Monitoring Program at AdventHealth for Children was developed for babies with single ventricle-type congenital heart disease to help anticipate any potential issues and provide support through the vulnerable period between discharge from the hospital and the Glenn operation. (adventhealth.com)
DORV15
- Double outlet right ventricle (DORV) is a form of congenital heart disease where both of the great arteries connect (in whole or in part) to the right ventricle (RV). (wikipedia.org)
- Double outlet right ventricle (DORV), as depicted in the image below, is a type of ventriculoarterial connection in which both the aorta (AO) and pulmonary artery (PA) arise entirely or predominantly from the right ventricle (RV). (medscape.com)
- Double outlet right ventricle (DORV) with transposition of the great arteries accounts for 26% of cases of DORV. (medscape.com)
- Electrocardiographic findings are rarely diagnostic for double outlet right ventricle (DORV). (medscape.com)
- [ 11 ] Of the 12 infants in whom double outlet right ventricle (DORV) was diagnosed and confirmed with angiography, 11 previously received a diagnosis based on subxiphoid two-dimensional echocardiography. (medscape.com)
- If you have DORV you have one big ventricle instead of two and blood travels from the heart in all directions. (lhm.org.uk)
- Double outlet right ventricle (DORV) is a congenital heart defect that occurs when the aorta and the main pulmonary artery both connect to the right ventricle instead the aorta connecting to the left ventricle. (umms.org)
- In double outlet right ventricle (DORV), both the aorta and pulmonary valve connect to the right ventricle. (msdmanuals.com)
- 2003 ). DORV is a congenital cardiac malformation in which both pulmonary artery and aorta predominantly arise from the right ventricle, and ventricular septal defect (VSD) always coexists (Lev et al. (springeropen.com)
- The term double outlet right ventricle (DORV) refers to a heterogeneous series of associated cardiac anomalies that involve the right ventricular outflow tract in which both of the great arteries arise entirely or predominantly from the right ventricle. (medscape.com)
- Double outlet right ventricle (DORV) is a complex cardiac malformation in which the majority of both pulmonary and aortic trunks arise from the right ventricle, typically coexisting with a VSD. (mhmedical.com)
- Double outlet right ventricle (DORV) refers to a congenital cardiac malformation in which most of the pulmonary artery and the aorta arise from the right ventricle, one subtype of which is known as the Taussig-Bing heart. (mhmedical.com)
- The surgical definition of DORV requires that at least 90% of the area of the outflow tracts arise from the right ventricle. (mhmedical.com)
- Therefore, cases of tetralogy of Fallot (see Chapter 52 ) in which the majority of the aortic outflow tract arises from the right ventricle could also be defined as DORV. (mhmedical.com)
- BACKGROUND: Atrioventricular septal defect (AVSD) and double outlet right ventricle (DORV) with normally related great arteries and normal ventricular sizes are associated with a good long-term prognosis after biventricular (BV) repair. (mcmaster.ca)
Connected to the right ventr1
- In a normal heart, the pulmonary artery is connected to the right ventricle and the aorta is connected to the left ventricle. (anavara.com)
Injected from the right ventricle1
- Most of the aorta arises from the right ventricle, the volume of venous blood was injected from the right ventricle into the aorta, which decided the oxygen saturations. (springeropen.com)
Transposition6
- Regardless of the end of the clinical spectrum (tetralogy of Fallot [TOF] or transposition of the great arteries [TGA]) at which double outlet right ventricle occurs, findings on anteroposterior and lateral chest radiography depend on the degree of pulmonary (or subpulmonary) stenosis. (medscape.com)
- Transposition of the Great Arteries (TGA) Transposition of the great arteries (in this case, dextro-transposition) occurs when the aorta arises directly from the right ventricle and the pulmonary artery arises from the left ventricle. (msdmanuals.com)
- The anatomic dysmorphology of double outlet right ventricle can vary from that of tetralogy of Fallot (TOF) on one end of the spectrum to complete transposition of the great arteries (TGA) on the other end (see the image below). (medscape.com)
- Brain Abscess in an Adult with Unrepaired Double-Outlet Right Ventricle with Transposition of Great Arteries and Pulmonic Stenosis. (escardio.org)
- The most common congenital diagnoses were Tetralogy of Fallot (n = 11), congenitally corrected transposition of the great arteries (ccTGA) (n = 9) and double outlet right ventricle (n = 6). (nih.gov)
- Transposition of the great arteries is when the pulmonary artery (the blood vessel that carries blood from the right ventricle to the lungs) is switched in position with the aorta (the blood vessel that carries blood from the left ventricle to the body). (federalwaypediatrics.com)
Tetralogy1
- [9] Cardiac defects can include Tetralogy of Fallot, aortic arch interruption, double outlet right ventricle with arch vessel abnormalities, and atrioventricular septal defects (AVSD). (aao.org)
Outflow tract3
- Attempts have been made to define the malformation based on the relative area of each outflow tract arising from the right ventricle, with an anatomic threshold of 50% being used. (mhmedical.com)
- The right ventricle discharges blood into the pulmonary artery across the pulmonic (semilunar) valve located in the outflow tract (infundibulum). (medscape.com)
- The inflow tract (sinus) and outflow tract (infundibulum) of the right ventricle are widely separated. (medscape.com)
Ventricular Septum2
- Its posterior wall is formed by the [[ventricular septum]], which bulges into the right ventricle, so that a transverse section of the cavity presents a semilunar outline. (wikidoc.org)
- However, because the surface of the right ventricle is trabecular, small defects of the muscular portion of the ventricular septum may be difficult to see. (medscape.com)
Anatomic3
- MRI is useful to obtain additional anatomic information, such as the relationship of both ventricles. (medscape.com)
- Demir MT, Amasyall Y, Kopuz C, Aydln ME, Corumlu U. The double outlet right ventricle with additional cardiac malformations: an anatomic and echocardiographic study. (medscape.com)
- Double outlet ventricles: review of anatomic and imaging characteristics. (nih.gov)
Predominantly2
- However, the Congenital Heart Surgery Nomenclature and Database Project defines double outlet right ventricle as a type of ventriculoarterial connection in which both great vessels arise either entirely or predominantly from the right ventricle. (medscape.com)
- Double outlet left ventricle (DOLV) is a rare congenital cardiac malformation in which both the pulmonary artery and the aorta arise exclusively or predominantly from the morphologic left ventricle. (hacettepe.edu.tr)
Great arteries5
- Echocardiography can be used to correctly identify the relative position of the great arteries, the degree of subsemilunar narrowing, the position of the ventricular septal defect (VSD), and the status of the mitral valve and left ventricle. (medscape.com)
- In 1793, Aberanthy described a heart with the origin of both great arteries from the right ventricle. (medscape.com)
- In general, from a surgical perspective, defining the lesion as double outlet right ventricle is reasonable when more than 50% of both of the great arteries arise from the right ventricle. (medscape.com)
- Based on the location of ventriculoseptal defect (VSD) in relation to great arteries, double outlet right ventricle can be classified into 4 main categories: double outlet right ventricle with subaortic VSD, double outlet right ventricle with subpulmonary VSD, double outlet right ventricle with doubly committed VSD, and double outlet right ventricle with noncommitted VSD. (medscape.com)
- We describe a case of DOLV with situs solitus, d-loop ventricles, d-malposition of the great arteries (S, D, D), severe pulmonary stenosis, and a subaortic ventricular septal defect in which the left ventricle was also severely hypoplastic. (hacettepe.edu.tr)
Cardiac3
- Cardiac catheterization, once the criterion standard for confirming double outlet right ventricle, is now rarely required in the evaluation or preoperative planning of this cardiac disorder. (medscape.com)
- [ 12 ] A study that assessed the incidence and diagnostic accuracy of preoperative cardiac CT scanning for identifying detailed coronary artery anatomy in 318 children with TOF or Fallot type of double outlet right ventricle found a 95% concordance between cardiac CT scanning and surgical findings, and a 96.9% diagnostic accuracy for cardiac CT scanning. (medscape.com)
- Coronary sinus, normally located between the LEFT ATRIUM and LEFT VENTRICLE on the posterior surface of the heart, can serve as an anatomical reference for cardiac procedures. (bvsalud.org)
Defects3
- The clinical manifestations are similarly variable, depending on how the anatomical defects affect the physiology of the heart, in terms of altering the normal flow of blood from the RV and left ventricle (LV) to the aorta and pulmonary artery. (wikipedia.org)
- Some of the heart defects involve structures within the heart itself, such as the two lower chambers of the heart (the ventricles) or the valves that control blood flow through the heart. (medlineplus.gov)
- Ventricular septal defects (VSDs) commonly occur in the area between the sinus and the outlet tract of the right ventricle. (medscape.com)
Left14
- The only outlet from the left ventricle (LV) is a ventricular septal defect (VSD) . (medscape.com)
- The only outflow from the left ventricle (LV) is a ventricular septal defect (VSD), which diverts blood toward the RV. (medscape.com)
- Common findings in a child with double outlet right ventricle include right ventricular hypertrophy, right axis deviation, and, occasionally, evidence of left ventricular hypertrophy. (medscape.com)
- Create a tunnel through the hole in the heart to connect the left ventricle to the aorta. (sparrow.org)
- Some adults born with double-outlet right ventricle need medicine to help the right or left lower heart chambers work better. (sparrow.org)
- Because both great vessels arise from one ventricle, there is some degree of mixing of desaturated systemic venous blood and highly saturated pulmonary venous return that enters the right ventricle via flow through the left atrium, left ventricle, and VSD. (msdmanuals.com)
- Although hearts with atrioventricular discordance (ie, congenitally corrected TGA) or univentricular atrioventricular connections (ie, double inlet left ventricle) can be correctly grouped in this spectrum of anomalies, this article focuses on only those hearts with atrioventricular concordance and 2 functional ventricles. (medscape.com)
- In this variant of double outlet right ventricle, the pulmonary artery preferentially receives left ventricular oxygenated blood, and the desaturated blood from the right ventricle streams to the aorta (TGA type). (medscape.com)
- This causes oxygen-rich blood to flow from the left ventricle to the right ventricle and mix with oxygen-poor blood. (anavara.com)
- The outcome of cases with a borderline small left ventricle (bLV) is unclear. (mcmaster.ca)
- Many morphologic variations of this malformation have been described but to the our knowledge DOLV with a hypoplastic left ventricle has not been reported before. (hacettepe.edu.tr)
- A hole in the wall between the right and left lower heart chambers, or the ventricles. (vejthani.com)
- The cavity equals in size that of the left ventricle, and is capable of containing about 85 c.c. (wikidoc.org)
- Medial rotation from the left exposes the left ventricle apex, left pulmonary veins, and left atrium. (medscape.com)
Arise2
- The aorta (AO) is anterior and to the right of the pulmonary artery (PA), and both arteries arise from the right ventricle (RV). (medscape.com)
- All of one vessel and most of the remaining vessel typically arise from the right ventricle. (medscape.com)
Taussig-Bing1
- The Taussig-Bing anomaly is a typical example of double outlet right ventricle with subpulmonary VSD. (medscape.com)
Right atrium2
- The structures initially seen from this perspective include the superior vena cava, right atrium, right ventricle, pulmonary artery, and aorta. (medscape.com)
- The right ventricle receives blood from the right atrium across the tricuspid valve, which is located in the large anterolateral (ie, sinus) portion of the right ventricle. (medscape.com)
Lethality1
- Mice homozygous for a knock-out allele exhibit a hypocellular placenta, abnormal placental labyrinth vasculature morphology, abnormal spongiotrophoblast inclusions, double outlet right ventricle, and partial lethality throughout fetal growth and development. (jax.org)
Endocardial1
- Essential modifiers of double outlet right ventricle: Revisit with endocardial surface images and 3-dimensional print models. (msdmanuals.com)
Diagnosis of double1
- MRI has been used in the diagnosis of double outlet right ventricle, but it is not yet a routine or well-established diagnostic modality forthis condition. (medscape.com)
Definition1
- The definition of a double outlet right ventricle has been a point of controversy among professionals in the field of congenital heart surgery. (medscape.com)
Occurs2
- In cases of a subaortic VSD, which occurs in 60-70% of patients, the VSD is closer to the aortic valve, thus oxygenated blood from the LV is directed to the AO and desaturated blood from the right ventricle (RV) is directed primarily to the PA (see the image below). (medscape.com)
- Not only was Claire born small, but she was also born with a type of congenital heart disease called double outlet right ventricle - a condition that occurs once in every 6,000 to 10,000 births, when the aorta and the pulmonary artery connect to the heart's ventricle. (childrensnational.org)
Blood vessel2
- Insert a blood vessel to connect the right ventricle to the pulmonary artery. (sparrow.org)
- Defined as the aorta (the blood vessel that pumps blood from the heart to the body) attaching to the right ventricle (the heart chamber that pumps blood from the right side of the heart to the lungs). (federalwaypediatrics.com)
Incidence1
- In the United States, the incidence of double outlet right ventricle is 0.09 cases per 1000 live births. (medscape.com)
Babies3
- In babies with double-outlet right ventricle, both the aorta and the pulmonary artery connect partially or completely to the right lower heart chamber. (sparrow.org)
- Babies with double-outlet right ventricle also have a hole between the lower heart chambers. (sparrow.org)
- Some babies with double-outlet right ventricle need heart repair surgery within the first few days of birth. (sparrow.org)
Chambers4
- The lower heart chambers are called the ventricles. (sparrow.org)
- In people with double-outlet right ventricle, there is also a hole between the lower heart chambers (ventricles), called a ventricular septal defect (VSD), which can be located in several places in the wall between the ventricles. (anavara.com)
- A double outlet right ventricle with a ventricular spetal defect (a hole between the two bottom chambers (ventricles) of the heart), that is considered to be closely related to the pulmonary origin. (nih.gov)
- A ventricular septal defect is when there is a hole between the two ventricles, which are the bottom two chambers of the heart. (federalwaypediatrics.com)
Fallot1
- Preoperative CT scanning is potentially useful for identifying coronary artery anatomy in children with TOF or Fallot type of double outlet right ventricle. (medscape.com)
Surgery1
- The shunt is removed later in life during heart surgery to repair the double-outlet right ventricle. (sparrow.org)
Disorders1
- Of these 3 subdivisions, the conal septum is clinically significant because it can be malpositioned in patients with congenital disorders (eg, double outlet right ventricle ). (medscape.com)
