Slit Ventricle Syndrome

Shunt9

• Linder M, Diehl J, Sklar FH: Subtemporal decompressions for shunt dependent ventricles: mechanism of action. (karger.com)
• Respondents were asked 13 multiple-choice and free-response questions regarding 4 fundamental problems encountered in shunted-hydrocephalus management: shunt malfunction, chronic cerebrospinal fluid (CSF) overdrainage, chronic headaches, and slit ventricle syndrome (SVS). (thejns.org)
• After ETV, there was no long-term morbidity whereas 61% patients of VP shunt continued to have some or other problem in the form of shunt obstruction, infection, new-onset seizures or slit ventricle syndrome. (iospress.com)
• Shunt freedom in slit ventricle syndrome: using paradoxical ventriculomegaly following lumbar shunting to our advantage. (ucsd.edu)
• Slit or small ventricles in the child with a shunt can be associated with high, low, or normal ICP and can be symptomatic or asymptomatic . (symptoma.com)
• The slit ventricle syndrome is intimately related with the entity of shunt over-drainage, although who's the definition of the former is implicated by a lack of universally accepted inclusion criteria. (bvsalud.org)
• OBJECTIVE: Slit ventricle syndrome (SVS) is an iatrogenic disease occurring in patients with ventriculoperitoneal shunt. (bvsalud.org)
• Staged reconstruction, including a Norwood plus right ventricle-to-pulmonary artery shunt (RVPAS) or modified Blalock-Taussig shunt (MBTS) procedure at the time of birth, a stage II superior cavopulmonary connection, and a completion Fontan, remain the mainstay of the treatment of functional single right ventricle lesions. (medscape.com)
• [ 4 ] The procedure has been technically refined over the years, but the essential components remain (1) atrial septectomy, (2) anastomosis of the proximal pulmonary artery to the aorta with homograft augmentation of the aortic arch, and (3) aortopulmonary (modified Blalock-Taussig shunt [MBTS]) shunt or right ventricle-to-pulmonary artery shunt (RVPAS) to provide restricted pulmonary blood flow. (medscape.com)

Floor of the third ventricle2

• Use a blunt instrument to penetrate the floor of the third ventricle. (medscape.com)
• Typically, SSCs expand from the prepontine space, displacing the floor of the third ventricle upwards, the pituitary stalk and optic chiasm upwards and forwards, and the mammillary bodies upwards and backwards. (biomedcentral.com)

Hydrocephalus5

• Postoperative spinal adhesive arachnoiditis presenting with hydrocephalus and cauda equina syndrome. (saintluc.be)
• The objective of this study was to determine whether neuronavigation-guided free-hand placement of ventricular catheters is an effective adjunct for children with hydrocephalus and small ventricles. (tau.ac.il)
• Lumboperitoneal shunts are used in communicating hydrocephalus, especially if ventricles are small. (medscape.com)
• Idiopathic intracranial hypertension (IIH) , also known as pseudotumor cerebri, is a syndrome with signs and symptoms of increased intracranial pressure but where a causative mass or hydrocephalus is not identified. (radiopaedia.org)
• As the cyst increases in size it fills and occludes the third ventricle, and distorts and blocks the aqueduct, which finally results in hydrocephalus. (biomedcentral.com)

Right ventricle7

• Other closely related functional single right ventricle lesions include double-outlet right ventricle with mitral atresia and unbalanced atrioventricular septal defect. (medscape.com)
• A common physiology of HLHS is that the systemic circulation is driven by the right ventricle via a patent ductus arteriosus. (medscape.com)
• however, surgical palliation, also referred to as staged reconstruction, can be undertaken in a series of surgical procedures that ultimately result in the right ventricle supporting the cardiac output to both the systemic and pulmonary circuits that are connected in series. (medscape.com)
• Staged surgical palliation of HLHS with a Fontan operation using the right ventricle as the systemic ventricle was first reported in 1983 by Norwood et al. (medscape.com)
• Norwood's strategy of creating a functional single right ventricle circulation initially involved an aortic-to-pulmonary artery connection with patch aortic arch reconstruction to form a neoaorta and controlled pulmonary blood flow with a RVPAS. (medscape.com)
• Third, they sever the Pulmonary Artery, sew shut the side opposite the heart, and sew the newly enlarged Aorta onto valve the Pulmonary Artery used to attach to.Finally, they install a gore- tex tube from inside the right ventricle and attach it to the Pulmonary Artery. (blogspot.com)
• Our son Tyson has Hypoplastic Right Ventricle, as well 3 other heart defects and 2 holes in the heart. (blogspot.com)

Lateral ventricle2

• The proximal catheter tip should lie anterior to the choroid plexus in the frontal horn of the lateral ventricle when the parietooccipital approach is used. (medscape.com)
• The atrium is the point of confluence between the occipital horn, inferior horn, and the body of the lateral ventricle and is the largest, most easily identifiable portion of the lateral ventricle. (davidleep.com)

Noncompliant1

• Buxton N, Punt J: Subtemporal decompression: the treatment of noncompliant ventricle syndrome. (karger.com)

Cerebrospinal fluid1

• With this condition, cerebrospinal fluid builds up in the ventricles of the brain. (lluch.org)

Symptomatic3

• Possible overlap between reversible cerebral vasoconstriction syndrome and symptomatic vasospasm after aneurysmal subarachnoid hemorrhage. (saintluc.be)
• Two (5.3%) patients developed symptomatic slit ventricles and 13.2% patients had new-onset seizures. (iospress.com)
• We conducted a retrospective evaluation of the safety, effectiveness, and long-term outcome of endoscopic aqueductoplasty and stent placement, performed in 18 consecutive patients with symptomatic TFV through a trans-fourth ventricle approach between 1994 and 2010. (neurologyindia.com)

Obstruction1

• Hypoplastic left heart syndrome (HLHS) is a spectrum of congenital heart defects that is characterized by hypoplasia of the left ventricle and multilevel obstruction of systemic cardiac output from the level of the mitral valve to the proximal descending thoracic aorta. (medscape.com)

Hypoplastic left hea3

• The term hypoplastic left heart syndrome (HLHS) was introduced by Noonan and Nadas in 1958 to describe the morphologic features of combined aortic atresia and mitral atresia. (medscape.com)
• The first successful palliation of hypoplastic left heart syndrome was reported by Norwood et al in a series of infants who underwent surgery from 1979-1981. (medscape.com)
• Travis Gary DiCarlo, first son of Roger and Nicole DiCarlo, was born at San Diego Kaiser Hospital, October 23, 2009 with a Congenital Heart Defect known as Hypoplastic Left Heart Syndrome, or HLHS. (blogspot.com)

Seizures1

• Less frequent features associated with the syndrome may include antimongoloid (upslanting) palpebral fissures (eye slits), high-arched palate, joint hyperextensibility, pectus excavatum (caved-in chest), strabismus , amblyopia , seizures, and mental retardation . (en-academic.com)

Cardiac1

• Atherosclerotic plaque rupture is the leading cause of cardiovascular death resulting from acute coronary syndrome (ACS) and leads to cardiac remodeling and fibrosis following ACS. (archivesofmedicalscience.com)

Headaches1

• The role of psychological factors in immune disorders and cancer, headaches and migraine, obesity, fibromyalgia, chronic fatigue syndrome , and premenstrual syndrome also are included. (symptoma.com)

Frontal1

• In 'lobar HPE,' the ventricles are separated, but there is incomplete frontal cortical separation (Corsello et al. (nih.gov)

Examination1

• Depending on our own expertise, histopathology of the treated cornea is actually confirmative in terms of the standard examination associated with eye diseases by simply slit-lamp remark in the Its polar environment as well as in many cases can help examine borderline outcomes. (bace-signal.com)

Cerebral Ventricles1

• The macrocephaly occurs without enlargement of the cerebral ventricles. (en-academic.com)

Entity1

• Slit ventricle syndrome remains a complex entity presenting a considerable challenge to treat successfully. (karger.com)

Autosomal2

• Inheritance of the syndrome is as an autosomal dominant trait. (en-academic.com)
• Fraser syndrome is an autosomal recessive malformation disorder characterized by cryptophthalmos, syndactyly, and abnormalities of the respiratory and urogenital tract (summary by van Haelst et al. (nih.gov)

Distinct2

• See Bowen syndrome (211200) for a comparable but probably distinct syndrome of multiple congenital malformations. (nih.gov)
• 1976) suggested that 2 distinct syndromes are subsumed under the designation pachyonychia congenita. (findzebra.com)

Functional1

• Our psychosocial model that includes four psychosocial factors and our five-step treatment program for patients with functional somatic syndromes are presented . (symptoma.com)

Genetic1

• Bannayan syndrome, a genetic disease characterized by macrocephaly (enlarged head), multiple lipomas (benign fatty tumors) and hemangiomas (benign blood vessel tumors). (en-academic.com)

Chronic3

• Lastly, there were variable opinions on the etiology of slit ventricle syndrome (SVS), which included early shunting, chronic overdrainage, and/or loss of brain compliance. (thejns.org)
• One such example is chronic fatigue syndrome , which in the past was considered by many to be psychosomatic, especially in women. (symptoma.com)
• Chronic intracranial hypertension is present with the prevalence of 30-40% in syndrome craniosynostoses, of 12-20% in monosynostoses. (csnn.eu)

Symptoms1

• syndrome - The aggregate of symptoms and signs associated with any morbid process, and constituting together the picture of the disease. (en-academic.com)

Treatment3

• Olson S: The problematic slit ventricle syndrome: a review of the literature and proposed algorithm for treatment. (karger.com)
• Treatment The management of slit ventricle syndrome is difficult and challenging. (symptoma.com)
• Our experience and the literature review suggest that endoscopic trans-fourth ventricle aqueductoplasty and stent placement is a minimally invasive, safe, and effective technique for the treatment of TFV and should be strongly recommended, especially in patients with supratentorial slit ventricles. (neurologyindia.com)

Placement1

• Object: Accurate placement of ventricular catheters in children with small ventricles can be difficult. (tau.ac.il)

Patients2

• Patients were excluded if alternative diagnoses such to here as multisystem inflammatory syndrome in adults as bacterial sepsis were identified. (cdc.gov)
• Fifteen patients presented with slit supratentorial ventricles. (neurologyindia.com)

Left3

• Impact of early hemispherotomy in a case of Ohtahara syndrome with left parieto-occipital megalencephaly. (saintluc.be)
• The CTPA demonstrated no PE, however there was extensive pulmonary airspace shadowing in both lower lobes consistent with acute respiratory distress syndrome (ARDS), as well as a highly abnormal appearance to the left atrium with a smooth margined filling defect extending from the posterior wall anteriorly compressing the lumen. (biomedcentral.com)
• But without a left ventricle, Travis' heart can't work that way. (blogspot.com)

Disease2

• A different mutation in PTEN causes Cowden disease which is a syndrome of multiple hamartomas (malformations resembling tumors composed of mature tissues), especially of the skin, mucous membranes, breast and thyroid. (en-academic.com)
• The syndrome is named after the Jerusalem-born American pathologist George A. Bannayan who described a case with the disease in 1971. (en-academic.com)

Disorders1

• But this condition is common in many known disorders, such as Down syndrome. (lluch.org)

Small2

• Four children were diagnosed as suffering from slit ventricle syndrome and 5 children had small to mildly dilated ventricles. (tau.ac.il)
• Conclusion: The usage of a neuronavigation system is safe and may be beneficial for optimal postioning and trajectory of ventricular catheters in children with small ventricles or an abnormal ventricular anatomy. (tau.ac.il)

Single3

• A multi-institutional, prospective, randomized, controlled trial (Single Ventricle Reconstruction or SVR trial) in 2005 compared the RVPAS to the MBTS. (medscape.com)
• In the most severe form, 'alobar HPE,' there is a single ventricle and no interhemispheric fissure. (nih.gov)
• In 'semilobar HPE,' the most common type of HPE in neonates who survive, there is partial cortical separation with rudimentary cerebral hemispheres and a single ventricle. (nih.gov)

Result2

• Синдроми хромосомної делеції Chromosomal deletion syndromes result from loss of parts of chromosomes. (msdmanuals.com)
• The disadvantages of epidural anaesthesia are that a few wom en com plain of dizziness or shivering, and that it m ay increase the length of the second stage and result in a rise in operative vaginal deliveries. (dnahelix.com)

Similar1

• In 1960 Harris D. Riley and William R. Smith had reported the same (or a remarkably similar) syndrome in a mother and 4 of her 7 offspring. (en-academic.com)

Brain1

• All brain ventricles are candidates for shunting. (wikipedia.org)

Past1

• Different surgical approaches have been described in the past to treat a trapped fourth ventricle (TFV) but, unfortunately, these techniques showed a high rate of dysfunction and complications. (neurologyindia.com)

Space1

• The surgeon forms a pocket beneath the epicranial aponeurosis (the subgaleal space) and allows CSF to drain from the ventricles, creating a fluid-filled swelling on the baby's scalp. (wikipedia.org)

Effects1

• Histopathology with the cornea as well as the regular slit-lamp microscope evaluation of cornael effects is executed routinely inside Its polar environment tests from our Institute, making use of a couple of common stainings (H&E and PAS). (bace-signal.com)